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Article
Lymphocyte phosphorylase kinase activities in the sex-linked form of liver phosphorylase kinase deficiency
Lymphocyte phosphorylase kinase activities were measured in normal controls and in patients with the sex-linked form of liver phosphorylase kinase deficiency. The reaction due to phosphorylase kinase activity ...
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Article
Glomerular electron-dense deposits in childhood IgA nephropathy
An electron-microscopic study of the glomeruli was made on 154 children with IgA nephropathy and no evidence of systemic disease, in whom immunofluorescence microscopy had shown diffuse mesangial deposition of...
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Article
Patents and literature
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Article
Phase transitions in the hydroquinone hydrogen sulfide clathrate compound
Heat capacities of [C6H4(OH)2]3·(H2S) x were measured between 1 and 15 K. Heat capacity peaks were found at (7.56±0.09) K, (7.61±0.05) K, and (7.65±0.07) K for the compounds wit...
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Article
Transient hyperphenylalaninaemia with a high neopterin to biopterin ratio in urine
A case of transient hyperphenylalaninaemia with a maturational delay of dihydropteridine synthesis is described. With the Guthrie test, the patient showed a blood phenylalanine level of 38 mg dl−1, which had fall...
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Article
Adrenoleukodystrophy without adrenal insufficiency and its magnetic resonance imaging
Fatty acids of plasma and erythrocyte membrane sphingomyelin were determined by gas chromatography-mass spectrometry in adrenoleukodystrophy (ALD) without adrenal insufficiency. Mass chromatogram tracing with ...
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Chapter and Conference Paper
Amino Acid Sequencing of Peptide Mixture: Structural Analysis of Human Hemoglobin Variants (Digit Printing Method)
Two strategies for determining the amino acid sequence of abnormal peptide containing amino acid substitution were developed. One is the mass spectrometric analysis of the peptide mixtures obtained by differen...
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Article
Experimental study on pathogenesis of the fetal brain damage by acute carbon monoxide intoxication of the pregnant mother
The pathogenesis of fetal brain damage caused by acute maternal carbon monoxide (CO) intoxication was experimentally investigated in cats; 11 pregnant cats in various gestational stages were exposed to 0.2–0.3...
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Article
Immunoelectron microscopic study of childhood IgA nephropathy and Henoch-Schönlein nephritis
Renal biopsy specimens from 11 children with Henoch-Schönlein nephritis and 14 with IgA nephropathy were examined by immunoelectron microscopy. The distribution of IgA reaction product (RP) was found to be sim...
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Article
Strengthening of nickel -base superalloys for nuclear heat exchanger application
Strengthening mechanisms of nickel-base superalloys have been discussed with the background of the Japanese research and development activities in this field. As candidates for materials of intermediate heat e...
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Article
Calorimetric study ofβ-cyclodextrin undecahydrate
Heat capacities of crystallineβ-cyclodextrin undecahydrate have been measured in the temperature range between 13 and 300K by use of a miniaturized adiabatic low-temperature calorimeter. A first-order phase trans...
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Article
Citrullinaemia: an infantile form withp-hydroxyphenylpyruvic andp-hydroxyphenyllactic acidurias
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Article
Regional cerebral blood flow of acute carbon monoxide poisoning in cats
The mechanism of selective vulnerability of the cerebral white matter and pallidum in acute carbon monoxide (CO) poisoning was experimentally investigated by measuring regional cerebral blood flow (rCBF) with ...
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Chapter and Conference Paper
Multiple ionization by energetic heavy ion collisions — an evidence of the innershell electron transfer in highly charged recoil ion production
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Article
Cockayne syndrome: Magnetic resonance images of the brain in a severe form with early onset
A 2-year-old boy with an early onset and severe form of Cockayne's syndrome (CS) showed differences from the common CS form, which made the clinical diagnosis difficult. However, the cellular characteristics o...
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Article
Calorimetric study on pure and KOH-doped argon clathrate hydrates
Pure and KOH (x=1.3×10−3)-doped argon clathrate hydrates were synthesized in an adiabatic high-pressure calorimetric cell from one mole of water and 200 MPa of Ar gas. The heat capacities of the hydrates were mea...
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Article
107: DETERMINATION OF SURFACTANT APOPROTEIN AND PHOSPHOLIPIDS IN AMNIOTIC FLUID FOR ESTIMATING FETAL LUNG MATURITY
Measurement of disaturated phosphatidylcholine(DSPC) or phosphatidylglycerol(PG) have been proved to be useful in complicated mothers for evaluating the fetal lung maturity. But the procedure is complicated an...
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Article
Serum arginine level in neonatal citrullinaemia
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Article
Micro-RBS Analysis of Masklessly Fabricated Structures
Rutherford backscattering (RBS) analysis of small-sized structures, fabricated by laser chemical vapor deposition (LCVD) with a focused laser beam and ion implantation with a focused ion beam (FIB), has been p...
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Article
Adult pigment type (Peiffer) of sudanophilic leukodystrophy
Two autopsy cases of siblings with the adult pigment (Peiffer) type of sudanophilic leukodystrophy (SLD), which demonstrated the full-blown stage (case 1) and early stage (case 2) of demyelination, were examin...
