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Article
An unusual kidney presentation of severe proteinuria in a 2-year-old girl: Questions
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Article
An unusual kidney presentation of severe proteinuria in a 2-year-old girl: Answers
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A cross-sectional study in patients with IgA nephropathy of correlations between clinical data and pathological findings at the time of renal biopsy: a Japanese prospective cohort study
The correlations between clinical data and pathological findings at the time of renal biopsy were investigated in IgA nephropathy patients.
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Article
Correction to: Validation of the diagnostic criteria for IgG4‑related kidney disease (IgG4‑RKD) 2011, and proposal of a new 2020 version
A correction to this paper has been published: https://doi.org/10.1007/s10157-021-02040-9
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Article
Concurrent minimal change disease and retroperitoneal liposarcoma successfully treated by tumor resection and steroid therapy
A 54-year-old Japanese woman developed simultaneous abdominal distension and bilateral leg edema. Her medical history and results of periodic medical check-up were unremarkable. Blood tests revealed severe hyp...
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Article
Two cases of idiopathic multicentric Castleman disease with nephrotic syndrome treated with tocilizumab
We report two cases of idiopathic multicentric Castleman disease (iMCD) with nephrotic syndrome (NS) treated with tocilizumab. Case 1 was a 58-year-old man diagnosed with iMCD prior to the onset of NS. Renal b...
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Article
Open AccessValidation of the diagnostic criteria for IgG4-related kidney disease (IgG4-RKD) 2011, and proposal of a new 2020 version
In 2011, the IgG4-related kidney disease (IgG4-RKD) working group of the Japanese Society of Nephrology proposed diagnostic criteria for IgG4-RKD. The aim of the present study was to validate those criteria an...
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Article
Open AccessIgM monoclonal gammopathy with heavy-and-light-chain amyloidosis resembling fibrillary glomerulonephritis determined by tandem mass spectrometry: a case report
Fibrillary glomerulonephritis (FGN) is distinguished from amyloidosis by thicker fibrils and the lack of staining with histochemical dyes typically reactive with amyloid. However, congophilic FGN has been prop...
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Article
A case of denosumab-associated membranous nephropathy in a patient with rheumatoid arthritis
We herein report a case of anti-RANKL monoclonal antibody-associated membranous nephropathy (MN). A 67-year-old woman with a history of rheumatoid arthritis treated with prednisolone and methotrexate for more ...
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Article
Open AccessClinicopathological characteristics of thrombospondin type 1 domain-containing 7A-associated membranous nephropathy
Thrombospondin type 1 domain-containing 7A (THSD7A) is a recently identified target antigen of idiopathic membranous nephropathy (iMN). The clinicopathological characteristics of THSD7A-associated MN are poorl...
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Article
Open AccessA grading system that predicts the risk of dialysis induction in IgA nephropathy patients based on the combination of the clinical and histological severity
Histological classification is essential in the clinical management of immunoglobulin A nephropathy (IgAN). However, there are limitations in predicting the prognosis of IgAN based on histological information ...
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Article
Focal segmental glomerulosclerosis with heterozygous apolipoprotein E5 (Glu3Lys)
Apolipoprotein (apo) E5 is a rare apoE isoform. The apoE5 (Glu3Lys) variant, which is caused by the substitution of lysine with glutamic acid at codon 3, has a relative frequency of 0.1% in Japan. Previous stu...
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Open AccessLong-term desensitization for ABO-incompatible living related kidney transplantation recipients with high refractory and rebound anti-blood type antibody: case report
ABO-incompatible living related kidney transplantation (ABO-iLKT) has increased the possibilities for kidney transplantation in patients with end stage renal disease. Due to advancements in immunosuppressive a...
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Article
Nationwide multicenter kidney biopsy study of Japanese patients with hypertensive nephrosclerosis
Nephrosclerosis is an increasingly reason for dialysis in Japan. However, kidney biopsy specimens for hypertensive nephrosclerosis are very limited; thus, the pathologic evaluation of hypertensive nephrosclero...
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Article
Clinicopathological analysis of biopsy-proven diabetic nephropathy based on the Japanese classification of diabetic nephropathy
The Japanese classification of diabetic nephropathy reflects the risks of mortality, cardiovascular events and kidney prognosis and is clinically useful. Furthermore, pathological findings of diabetic nephropa...
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Article
Reproducibility for pathological prognostic parameters of the Oxford classification of IgA nephropathy: the authors reply
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Tubulointerstitial nephritis as adverse effect of programmed cell death 1 inhibitor, nivolumab, showed distinct histological findings
Immune-checkpoint inhibitor nivolumab (anti-PD-1 antibody) blocks T cell inhibition and stimulate immunologic response toward cancer cells. It was also revealed that PD-1/PD-L1 interaction crucially controls t...
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Article
Open AccessFibronectin glomerulopathy complicated with persistent cloaca and congenital esophageal atresia: a case report and literature review
Fibronectin glomerulopathy is a rare, inherited, autosomal dominant, glomerular disease characterized by proteinuria, microscopic hematuria, hypertension, massive glomerular deposits of fibronectin, and slow p...
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Article
Reproducibility for pathological prognostic parameters of the Oxford classification of IgA nephropathy: a Japanese cohort study of the Ministry of Health, Labor and Welfare
The Oxford classification of IgA nephropathy (IgAN) was proposed by international working group in 2009. Interobserver reproducibility of each pathological definition was already evaluated, but that of four pa...
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Article
Open AccessEstimation of the number of histological diagnosis for IgG4-related kidney disease referred to the data obtained from the Japan Renal Biopsy Registry (J-RBR) questionnaire and cases reported in the Japanese Society of Nephrology Meetings
More than 2 years have passed since the proposal of the diagnostic criteria for IgG4-related kidney disease (IgG4-RKD). The aim of this study was to estimate the number of histological diagnosis for IgG4-RKD t...
