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Article
Open AccessImpact of gallbladder hypoplasia on hilar hepatic ducts in biliary atresia
Biliary atresia (BA) is an intractable disease of unknown cause that develops in the neonatal period. It causes jaundice and liver damage due to the destruction of extrahepatic biliary tracts,. We have found t...
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Article
Open AccessPostoperative pulmonary vascular growth in patients with congenital diaphragmatic hernia
Postoperative pulmonary growth in congenital diaphragmatic hernias (CDH) remains unclear. We investigated postoperative pulmonary vascular growth using serial lung perfusion scintigraphy in patients with CDH.
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Article
Influence of surgical volume on the mortality and morbidity of gastrointestinal perforation in children
To clarify the influence of surgical volume on the mortality and morbidity of gastrointestinal perforation in children in Japan.
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Article
Open AccessImpact of the novel coronavirus infection on pediatric surgery: an analysis of data from the National Clinical Database
The coronavirus disease 2019 (COVID-19) pandemic limited the delivery of medical resources. Although surgeries are triaged according to disease severity and urgency, a delay in diagnosis and surgery can be det...
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Article
Risk factors for postoperative anastomotic leakage after repair of esophageal atresia: a retrospective nationwide database study
Postoperative anastomotic leakage is the most frequent short-term complication of esophageal atresia repair in neonates. We conducted this study using a nationwide surgical database in Japan to identify the ri...
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Article
Open AccessA case of Hirschsprung’s disease with segmental dilatation of the colon
Segmental dilatation of the colon (SDC) is a rare disease that is characterized by an abrupt segment of dilated colon between regions of normal-sized colon. We herein report a case of SDC associated with Hirsc...
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Article
A case of right hypodysplastic kidney and ectopic ureter associated with bicornuate uterus in a prepubertal girl
Congenital anomalies of the kidney and urinary tract (CAKUT) are frequently associated with Mullerian anomalies. This can be explained by the fact that Mullerian duct elongation depends on the preformed Wolffi...
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Article
Perioperative outcomes of laparoscopically assisted anorectoplasty versus conventional procedures for anorectal malformation: a retrospective nationwide database study
This study aimed to compare the perioperative outcomes of laparoscopically assisted anorectoplasty (LAARP) and conventional procedures (CPs) for anorectal malformation (ARM) using a national inpatient database...
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Article
Open AccessIdentification of trypsin-degrading commensals in the large intestine
Increased levels of proteases, such as trypsin, in the distal intestine have been implicated in intestinal pathological conditions1–3. However, the players and mechanisms that underlie protease regulation in the ...
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Article
Laparoscopic approach for abdominal neuroblastoma in Japan: results from nationwide multicenter survey
Some neuroblastoma (NB) cases are suitable for minimally invasive surgery (MIS), but indication and technical issue are unclear. We assessed the current status of MIS for abdominal NB after mass screening peri...
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Article
Open AccessAureobasidium melanigenum catheter-related bloodstream infection: a case report
Aureobasidium melanigenum is a ubiquitous dematiaceous fungus that rarely causes invasive human infections. Here, we present a case of Aureobasidium melanigenum bloodstream infection in a 20-year-old man with lon...
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Article
Open AccessEctopic gallbladder with congenital biliary dilatation: a pediatric case report
An ectopic gallbladder is a rare anomaly and can result in the misinterpretation of imaging findings and clinical confusion. Knowledge of such anomalies facilitates accurate diagnoses and prompt management. We...
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Article
Laparoscopic Versus Open Appendectomy for Acute Appendicitis in Children: a Nationwide Retrospective Study on Postoperative Outcomes
Our aim was to compare postoperative outcomes of laparoscopic and open appendectomies for acute appendicitis in children under the circumstance of widespread use of laparoscopic surgery.
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Article
Open AccessA Japanese prospective multicenter study of urinary oxysterols in biliary atresia
Diagnosis of biliary atresia (BA) can involve uncertainties. In the present prospective multicenter study, we considered whether urinary oxysterols represent a useful marker for diagnosis of BA in Japanese chi...
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Article
Prophylactic innominate artery transection to prevent tracheoinnominate artery fistula: a retrospective review of single institution experiences
This study aimed to investigate the optimal indication and availability of prophylactic innominate artery transection (PIAT).
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Biliary Atresia: Signs and Symptoms, Prenatal Diagnosis
Common clinical signs and symptoms suggestive of biliary atresia include jaundice, acholic stool, dark urine, and hepatomegaly. While acholic, pale, or clay-colored stools are well-known signs of biliary atres...
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Article
Impact of congenital heart disease on outcomes after primary repair of esophageal atresia: a retrospective observational study using a nationwide database in Japan
To verify the association between congenital heart disease (CHD) and postoperative complications after primary repair of esophageal atresia in patients from a Japanese nationwide database.
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Article
Postoperative Small Bowel Obstruction Following Laparoscopic or Open Fundoplication in Children: A Retrospective Analysis Using a Nationwide Database
Postoperative small bowel obstruction (SBO) is one of the most serious adverse events resulting in deteriorated quality of life in children. Numerous studies have shown that laparoscopic surgery significantly ...
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Article
Outcomes of Alagille syndrome following the Kasai operation: a systematic review and meta-analysis
Infants with Alagille syndrome (AGS) frequently develop neonatal cholestasis, and some AGS infants who suspected of biliary atresia subsequently undergo the Kasai operation with the diagnosis of biliary atresi...
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Article
Clinical features and practice patterns of gastroschisis: a retrospective analysis using a Japanese national inpatient database
The number of infants with gastroschisis is increasing worldwide, but advances in neonatal intensive care and parenteral nutrition have reduced gastroschisis mortality. Recent clinical data on gastroschisis ar...
