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Imaging in the Evaluation of Children with Suspected Craniosynostosis

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Evidence-Based Imaging in Pediatrics

Part of the book series: Evidence-Based Imaging ((Evidence-Based Imag.))

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Abstract

Craniosynostosis is the premature fusion of one or more skull sutures. This results in deformity of the calvarium, which is one of the clinical manifestations of this pathology. These deformities follow certain predictable clinical characteristics depending on the suture(s) involved. The clinical manifestations range from cosmetic deformity to increased intracranial pressure placing the patient at risk for cognitive, visual, and hearing impairment [1, 2]. Craniosynostosis may be broadly grouped into syndromic and non-syndromic. Exact etiology is not fully understood although several genes have been found to be involved in the pathogenesis of syndromic cases [3–6].

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Authors and Affiliations

  1. Diagnostic Radiology, Nicklaus Children’s Hospital, Miami, FL, USA

    Enrique Alvarado

  2. Division of Neuroradiology-Neuroimaging, Department of Radiology, Nicklaus Children’s Hospital, Miami, FL, USA

    Enrique Alvarado & L. Santiago Medina

  3. Herbert Wertheim College of Medicine, Florida International University, Miami, FL, USA

    L. Santiago Medina

  4. Harvard Medical School, Boston, MA, USA

    L. Santiago Medina

Authors
  1. Enrique Alvarado
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  2. L. Santiago Medina
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Correspondence to Enrique Alvarado .

Editor information

Editors and Affiliations

  1. Department of Radiology, 3NW, Children's Hospital of Philadelphia, Philadelphia, PA, USA

    Hansel J. Otero

  2. Department of Radiology, 3NW, Children's Hospital of Philadelphia, Philadelphia, PA, USA

    Summer L. Kaplan

  3. Dept Of Radiology, MCH Radiology, Miami Children's Hospital, Miami, FL, USA

    L Santiago Medina

  4. Dept of Radiology, Virginal Mason Medical Center, Seattle, WA, USA

    C. Craig Blackmore

  5. Zionsville, IN, USA

    Kimberly E Applegate

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Alvarado, E., Medina, L.S. (2022). Imaging in the Evaluation of Children with Suspected Craniosynostosis. In: Otero, H.J., Kaplan, S.L., Medina, L.S., Blackmore, C.C., Applegate, K.E. (eds) Evidence-Based Imaging in Pediatrics. Evidence-Based Imaging. Springer, Cham. https://doi.org/10.1007/978-3-030-38095-3_4-1

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  • DOI: https://doi.org/10.1007/978-3-030-38095-3_4-1

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  • Print ISBN: 978-3-030-38095-3

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