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How personality influences health outcomes and quality of life in adult patients with cystic fibrosis
BackgroundThe present study evaluates personality traits in adult patients with cystic fibrosis (CF) and correlates these results with health-related...
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CT imaging shows specific pancreatic abnormalities in persons with cystic fibrosis related diabetes
Cystic fibrosis related diabetes (CFRD) is observed in 20–50% of adults with cystic fibrosis (CF). Pancreas abnormalities on imaging, e.g. pancreas...
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Non-invasive Ventilation in Adults with Cystic Fibrosis
NIV is used routinely in patients with cystic fibrosis despite the evidence in the literature supporting this practice being fairly limited. The main... -
Targeting ubiquitination machinery in cystic fibrosis: Where do we stand?
Cystic Fibrosis (CF) is a genetic disease caused by mutations in CFTR gene expressing the anion selective channel CFTR located at the plasma membrane...
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Increasing incidence rate of breast cancer in cystic fibrosis - relationship between pathogenesis, oncogenesis and prediction of the treatment effect in the context of worse clinical outcome and prognosis of cystic fibrosis due to estrogens
Cystic fibrosis (CF) is the most common genetic disease in the Caucasion population. Thanks to the CFTR modulators therapy, life expectancy will...
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Cystic fibrosis and CFTR-related disorder with electrolyte imbalance at diagnosis: clinical features and outcome in an Italian cohort
There is limited information available on the clinical data, sweat test trends, and outcomes of individuals with cystic fibrosis (CF) who present...
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Phenotypic and genotypic characteristics of Pseudomonas aeruginosa isolated from cystic fibrosis patients with chronic infections
Patients with cystic fibrosis are predisposed to chronic respiratory tract infections caused by Pseudomonas aeruginosa . As the disease progresses,...
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Anxiety, Cystic Fibrosis, and Organ Transplantation
The presence of an active anxiety disorder in patients under consideration for organ transplantation has the potential to significantly impact... -
Therapeutic applications of curcumin nanomedicine formulations in cystic fibrosis
Medicinal applications of turmeric-derived curcumin have been known to mankind for long ages. Its potential in managing “cystic fibrosis” has also...
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Chloride Activity Sensing in Sweat for Cystic Fibrosis Diagnosis by Biocompatible Flexible Tag
The pioneering design of a wearable miniaturized and flexible potentiometric chloride activity sensing platform to provide real-time diagnosis and... -
Incidence of nontuberculous mycobacteria infections among persons with cystic fibrosis in the United States (2010–2019)
BackgroundNontuberculous mycobacteria (NTM) are ubiquitous, environmental bacteria that can cause chronic lung disease. Persons with cystic fibrosis...
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Meconium Ileus and Surgical Features of Cystic Fibrosis
There are many surgical manifestations of cystic fibrosis with the gastrointestinal tract prominent. These include meconium ileus, meconium plug... -
Validation of TMEM16A Modulation as a Therapeutic Approach for the Treatment of Cystic Fibrosis: The Discovery of Novel TMEM16A Potentiators
The discovery of transmembrane member 16A (TMEM16A) as the molecular identity of Ca 2+-activated Cl− channels (CaCCs) has reignited interest in the... -
Mutational spectrum of CFTR in cystic fibrosis patients with gastrointestinal and hepatobiliary manifestations
BackgroundCystic fibrosis (CF) is a rare and debilitating autosomal recessive disorder. It hampers the normal function of various organs and causes...
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Cystic Fibrosis
A 3 year old girl is referred with nasal obstruction by the Paediatricians. She was born at term with rectal prolapse, and was found to carry the... -
Clinical significance of BPI-ANCA in patients with cystic fibrosis: a single center prospective study
Recurrent pulmonary exacerbation due to infection and inflammation remain the major cause of mortality and morbidity in patients with cystic fibrosis...
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Modelling and Design of an ISFET-Based NaCl Sensor for Cystic Fibrosis Diagnosis and Management
Ion-Sensitive Field-Effect Transistors (ISFETs) are widely used for detecting various target analytes in chemical and biological solutions. Although... -
SARS-CoV-2 viral entry and replication is impaired in Cystic Fibrosis airways due to ACE2 downregulation
As an inherited disorder characterized by severe pulmonary disease, cystic fibrosis could be considered a comorbidity for coronavirus disease 2019....
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Who Am I? Self-concept in Adults with Cystic Fibrosis: Association with Anxiety and Depression
Cystic Fibrosis (CF) is a progressive condition resulting in reduced lung function and strongly associated with elevated anxiety and depression...