Search
Search Results
-
Cystic Fibrosis
Cystic fibrosis (CF) is an inherited disease affecting multiple systems, which can result in progressive lung disease, pancreatic insufficiency,...
-
Cystic Fibrosis Transmembrane Conductance Regulator (CFTR)-Targeted Therapeutics for Cystic Fibrosis
Treatment of the common life-limiting genetic disease cystic fibrosis (CF) has been transformed by small molecule therapeutics that target the root...
-
Cystic Fibrosis Chronic Rhinosinusitis
Chronic rhinosinusitis (CRS) is a pervasive and challenging entity to treat in patients with cystic fibrosis (CF). CF CRS develops as a direct...
-
Cystic Fibrosis
Cystic fibrosis (CF) is an inherited multisystem disease. Pulmonary failure, liver cirrhosis, and pancreatic insufficiency, including CF-related...
-
Macrolides and Cystic Fibrosis
Macrolide antibiotics attracted interest as a potential therapy in cystic fibrosis (CF) due to remarkable similarities in pathogenic features with...
-
Cystic Fibrosis-related Diabetes
Cystic fibrosis (CF) is a genetic disorder that is primarily known to impact the lungs; however, many patients are also diagnosed with diabetes...
-
Cystic Fibrosis
The cystic fibrosis transmembrane regulator protein (CFTR) is a chloride and bicarbonate channel situated at the apical surface of secretory...
-
Cystic Fibrosis in Adults
Cystic fibrosis (CF) occurs due to a mutation in a single gene encoding the cystic fibrosis transmembrane conductance regulator protein (CFTR)...
-
Cystic Fibrosis Management in Develo** Countries
Cystic fibrosis (CF) is a genetic disorder that affects the respiratory and digestive systems, posing unique challenges in develo** countries. This...
-
Comparative microbiome analysis in cystic fibrosis and non-cystic fibrosis bronchiectasis.
BackgroundBronchiectasis is a condition characterized by abnormal and irreversible bronchial dilation resulting from lung tissue damage and can be...
-
Bioassays zur Quantifizierung der „cystic fibrosis transmembrane conductance regulator“-Funktion
Bioassays for the quantification of the cystic fibrosis transmembrane conductance regulator (CFTR) function play a crucial role in the diagnosis,...
-
Future therapies for cystic fibrosis
We are currently witnessing transformative change for people with cystic fibrosis with the introduction of small molecule, mutation-specific drugs...
-
Update on Cystic Fibrosis in Pediatric Patients
Purpose of ReviewCystic fibrosis is an inherited, multisystem disease that affects the gastrointestinal system in numerous ways. This article reviews...
-
Understanding CFTR Functionality: A Comprehensive Review of Tests and Modulator Therapy in Cystic Fibrosis
Cystic fibrosis is a genetic disorder inherited in an autosomal recessive manner. It is caused by a mutation in the Cystic Fibrosis Transmembrane...
-
Bronchiectasis in Children Unrelated to Cystic Fibrosis
Bronchiectasis is characterized by abnormal dilation of bronchi seen on high-resolution computed tomography (HRCT) as a result of damage in the...
-
Novel therapeutic approach for the treatment of cystic fibrosis based on freeze-dried tridrug microparticles to treat cystic fibrosis
BackgroundCystic fibrosis is a severe, autosomal recessive disease that shortens life expectancy. According to studies, approximately 27% of patients...
-
Microbiome in Cystic Fibrosis
Cystic fibrosis (CF) is a genetic disease caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene leading to the...
-
Cystic fibrosis transmembrane conductance regulator (CFTR): beyond cystic fibrosis
BackgroundThe cystic fibrosis transmembrane conductance regulator ( CFTR ) gene has been traditionally linked to cystic fibrosis (CF) inheritance in...
-
Depression, anxiety, and hopelessness in a sample of Egyptian children diagnosed with cystic fibrosis
BackgroundEven though current therapeutic approaches have significantly increased the longevity and standard of living for children suffering from...
-
The prevalence of developmental defects of enamel in people with cystic fibrosis: a systematic review
BackgroundOral health impacts systemic health, individual well-being, and quality of life. It is important to identify conditions that may exacerbate...
