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  1. No Access

    Article

    Body composition in young adults with inborn errors of protein metabolism—A pilot study

    The natural history of inborn errors of protein metabolism and the long-term effects of prescribed semisynthetic therapeutic diets are largely unknown. We assessed body composition, measuring body-fat mass and...

    G. Wilcox, B. J. G. Strauss, D. E. M. Francis… in Journal of Inherited Metabolic Disease (2005)

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    Article

    Splenectomy in two siblings with G-CSF-dependent glycogen storage disease type Ib

    A. Boneh, A. W. Auldist, D. E. M. Francis… in Journal of Inherited Metabolic Disease (2001)

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    Article

    Maternal tyrosinaemia II: Management and successful outcome

    A 25-year-old woman with tyrosinaemia type II was treated from the 5th week of pregnancy with a protein-restricted diet supplemented with a tyrosine/phenylalanine-free amino acid mixture. Tyrosine concentratio...

    D. E. M. Francis, D. M. Kirby, G. N. Thompson in European Journal of Pediatrics (1992)

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    Chapter

    Caloreen and Its Use in Sick Children

    This paper concerns the use of energy supplements for children in various clinical conditions. Children require a balanced diet containing the essential nutrients to keep well and growing; they have different ...

    D. E. M. Francis in Glucose Polymers in Health and Disease (1977)