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Article
Open AccessIntraoperative mechanical ventilation and incidence of pneumothorax in lymphangioleiomyomatosis
Patients with lymphangioleiomyomatosis (LAM) are considered high risk for most surgeries and require specific anesthetic considerations mainly because of the common spontaneous pneumothorax (PTX). To explore w...
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Article
Lack of CFAP54 causes primary ciliary dyskinesia in a mouse model and human patients
Primary ciliary dyskinesia (PCD) is a highly heterogeneous recessive inherited disorder. FAP54, the homolog of CFAP54 in Chlamydomonas reinhardtii, was previously demonstrated as the C1d projection of the central...
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Article
Open AccessEffects of COVID-19 infection in patients with autoimmune pulmonary alveolar proteinosis: a single-center study
Autoimmune pulmonary alveolar proteinosis (aPAP) is a rare interstitial lung disease. COVID-19 is associated with worse prognosis in previous lung diseases patients. But the prognosis of aPAP patients after in...
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Article
Experimental Study and Fine-Tuned Simulation of Cable-Joint Pair Slip** in the Cable-Supported Structure
During the tensioning process of the cable-supported structure, the sliding friction between cable wires and joint will have a great influence on the mechanical properties of the structure. However, due to the...
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Article
Humoral response to inactivated SARS-CoV-2 vaccines in patients on sirolimus alone
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Article
Open AccessGene mutations in sporadic lymphangioleiomyomatosis and genotype–phenotype correlation analysis
Sporadic lymphangioleiomyomatosis (S-LAM) is a rare neoplasm with heterogeneous clinical features that is conventionally considered to be related to TSC2. This study serves to elucidate the mutation landscape and...
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Article
Open AccessSirolimus reduces the risk of pneumothorax recurrence in patients with lymphangioleiomyomatosis: a historical prospective self-controlled study
Spontaneous pneumothorax has a high incidence and high rate of recurrence in patients with lymphangioleiomyomatosis (LAM). The risk factors for pneumothorax and the effects of sirolimus on pneumothorax in pati...
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Article
Open AccessThe etiology of diffuse cystic lung diseases: an analysis of 1010 consecutive cases in a LAM clinic
The differential diagnosis of diffuse cystic lung disease (DCLD) is a clinical challenge. We wish to analyze the distribution of the etiology of DCLD based on data from a single lymphangioleiomyomatosis (LAM) ...
