26 Result(s)

Article

Behandlung der Purpura-Schönlein-Henoch-Nephritis bei Kindern und Jugendlichen

Bei der Purpura Schönlein-Henoch findet sich häufig eine Nierenbeteiligung, die in ausgeprägten Fällen zu einer chronischen Niereninsuffizienz führen und eine dauerhafte Nierenersatztherapie notwendig machen k...

PD Dr. M. Pohl, K. Dittrich, J.H.H. Ehrich, B. Hoppe… in Monatsschrift Kinderheilkunde (2013)

Article

Urinproteomanalytik

Da Urin einfach und in großen Mengen gewonnen werden kann und sich in ihm viele Moleküle befinden, die Hinweise auf die Physiologie und Pathologie enthalten, ist er eine attraktive Quelle für klinische Proteom...

J.H.H. Ehrich, E. Schiffer, J. Drube in Der Urologe (2011)

Article

Lysosomale Transportdefekte

Angeborene lysosomale Speichererkrankungen sind gekennzeichnet durch intralysosomale Speicherung von Substanzen, die normalerweise in diesen Organellen ab- oder umgebaut werden. Auf molekularer Ebene beruhen d...

PD Dr. A. M. Das, S. Illsinger, J. H. H. Ehrich in Monatsschrift Kinderheilkunde (2006)

Article

Does growth hormone therapy harmonize distorted morphology and body composition in chronic renal failure?

Recombinant human growth hormone (rhGH) therapy of growth retardation in chronic renal failure (CRF) has become well established. While there are ample data about its effectiveness in restoring longitudinal gr...

M. Zivicnjak, D. Franke, J. H. H. Ehrich, G. Filler in Pediatric Nephrology (2000)

Article

Obstructive airway disease caused by Moraxella catarrhalis after renal transplantation

We report a case of severe acute obstructive airway disease 2 months after renal transplantation in a 16-year-old patient with Biedl-Bardet syndrome who was transplanted for end-stage renal failure secondary t...

Kathrin Seidemann, Melchior Lauten, Monika Gappa, Gisela Offner… in Pediatric Nephrology (2000)

Article

Manifestations and treatment of Schimke immuno-osseous dysplasia: 14 new cases and a review of the literature

Schimke immuno-osseous dysplasia (SIOD) is a rare autosomal recessive spondylo-epiphyseal dysplasia. The characteristic features of SIOD include 1) short stature with hyperpigmented macules and an unusual fac...

C. F. Boerkoel, S. O'Neill, J. L. André, P. J. Benke… in European Journal of Pediatrics (2000)

Article

Schönlein-Henoch-Nephritis

M. Kirschstein, J.H.H. Ehrich in Monatsschrift Kinderheilkunde (1998)

Article

Slowly deteriorating insulin secretion and C-peptide production characterizes diabetes mellitus in infantile cystinosis

Infantile cystinosis, a rare lysosomal storage disease of cystine, leads to Fanconi syndrome and end-stage renal failure. After renal transplantation, no recurrence of the disease occurs in the graft, but oth...

G. Filler, P. Amendt, M. A. von Bredow, W. Rohde… in European Journal of Pediatrics (1998)

Article

Clinical features of unilateral multicystic renal dysplasia in children

A clinical study of 204 patients with unilateral multicystic renal dysplasia referred to 30 nephrology departments was undertaken to assess the frequency of complications in children who underwent nephrectomy (n

S. Rudnik-Schöneborn, U. John, F. Deget, J. H. H. Ehrich… in European Journal of Pediatrics (1998)

Article

Dosing of MMF in combination with tacrolimus for steroid-resistant vascular rejection in pediatric renal allografts

Steroid-resistant vascular rejection was treated in seven adolescent renal allograft recipients using the combination of mycophenolate mofetil (MMF) and tacrolimus (FK506). Since there are no published pediat...

G. Filler, D. Lampe, I. Mai, J. Strehlau, J. H. H. Ehrich in Transplant International (1998)

Article

Nierenersatztherapie von osteuropäischen Kindern und Jugendlichen in Westeuropa Psychosoziale, medizinische und organisatorische Aspekte

I. Hirte, J. Gellermann, G. Filler, M. Zimmering… in Monatsschrift Kinderheilkunde (1998)

Article

Renal replacement therapy for end-stage renal failure before 2 years of age

J. H. H. Ehrich, G. Rizzoni, F. P. Brunner, W. Fassbinder… in Pediatric Nephrology (1993)

Article

The paediatric registry of the European Dialysis and Transplant Association: 20 years' experience

The first publication of the paediatric registry of the European Dialysis and Transplant Association appeared in 1971. Since then nearly 50 further articles have appeared and this paper provides a full bibliog...

M. Broyer, C. Chantler, R. Donckerwolcke, J. H. H. Ehrich… in Pediatric Nephrology (1993)

Article

Paediatric aspects of renal transplantation: experience of a single centre

G. Offner, P. F. Hoyer, J. H. H. Ehrich, R. Pichlmayr, J. Brodehl in Pediatric Nephrology (1993)

Article

Long versus standard prednisone therapy for initial treatment of idiopathic nephrotic syndrome in children

Two regimens of steroid treatment for the initial attack of idiopathic nephrotic syndrome (NS) in children were compared in a controlled prospective multicentre study. Long prednisone therapy consisted of 60 mg/m

J. H. H. Ehrich, J. Brodehl in European Journal of Pediatrics (1993)

Article

Partial and complete de Toni-Debré-Fanconi syndrome after ifosfamide chemotherapy of childhood malignancy

Ten out of 79 patients treated with ifosfamide (IFO) developed a complete (n = 2) or partial (n = 8) de Toni-Debré-Fanconi syndrome (RFS). All but one of these patients had been treated in addition with cisplatin...

R. Rossi, J. H. H. Ehrich in European Journal of Clinical Pharmacology (1993)

Article

Paediatric aspects of renal transplantation: Experience of a single centre

From 1970 to 1991 a total of 244 renal transplantations were performed in 203 children at the Medical School in Hannover. The mean patient age was 10.4 years with a range between 11 months and 16.9 years. Fift...

G. Offner, P. F. Hoyer, J. H. H. Ehrich, R. Pichlmayr… in European Journal of Pediatrics (1992)

Article

Kidney transplantation in primary oxalosis: data from the EDTA Registry

M. Broyer, F. P. Brunner, H. Brynger, S. R. Dykes, J. H. H. Ehrich… in Pediatric Nephrology (1991)

Article

Mitotic disturbance associated with mosaic aneuploidies

The association of various unsystematic aneuploidies with premature centromere division (PCD) was observed in a patient with conspicuous clinical features and combined immunodeficiency. Trisomies and monosomie...

K. Miller, W. Müller, L. Winkler, M. R. Hadam, J. H. H. Ehrich… in Human Genetics (1990)

Article

Cyclosporin a treatment in children with minimal change nephrotic syndrome and focal segmental glomerulosclerosis

In a pilot study 23 children with nephrotic syndrome were treated with cyclosporin A (Cs) for 6–45 months. 8 children suffered from steroid dependent minimal change nephrotic syndrome (MCNS) and had experience...

J. Brodehl, M. Brandis, U. Helmchen, P. F. Hoyer, R. Burghard… in Klinische Wochenschrift (1988)