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Biliary sepsis complication with congenital hepatic fibrosis: an unexpected outcome
BackgroundCHF (Congenital hepatic fibrosis) is a rare hereditary disease characterized by periportal fibrosis and ductal plate malformation. Little...
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Elderly onset congenital hepatic fibrosis with portal hypertension diagnosed after recurrent cholangitis: a case report
Congenital hepatic fibrosis is a rare autosomal recessive disorder caused by ductal plate malformation that can manifest as hepatic fibrosis alone or...
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Congenital hepatic fibrosis and its mimics: a clinicopathologic study of 19 cases at a single institution
BackgroundCongenital hepatic fibrosis (CHF) is a rare inherited form of ductal plate malformation associated with polycystic kidney disease. The...
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Liver cirrhosis: relationship between fibrosis-associated hepatic morphological changes and portal hemodynamics using four-dimensional flow magnetic resonance imaging
PurposeThe mechanisms underlying the morphological changes in liver cirrhosis remain unknown. This study aimed to clarify the relationship between...
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Congenital hepatic fibrosis with novel mutations in PKD1 gene masquerading as early cryptogenic cirrhosis: a rare case report
BackgroundCongenital hepatic fibrosis (CHF) is a rare disorder of the porto-biliary system occurring due to the defective remodeling of ductal...
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Spontaneous evolution patterns of focal congenital hepatic hemangiomas: a case series of 25 patients
BackgroundHepatic hemangiomas are the most common benign liver tumors of infancy. They are termed congenital if fully developed at birth or infantile...
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Endovascular management of a congenital hepatic arterioportal malformation in a low resource setting
BackgroundArterioportal malformations, a rare type of vascular malformation, have significant associated morbidity and mortality. Management requires...
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Noninvasive models for the prediction of liver fibrosis in patients with chronic hepatitis B
ObjectiveTo evaluate the diagnostic accuracy of aspartate aminotransferase(AST)/ alanine transaminase (ALT), AST to platelet ratio index (APRI),...
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Hepatic and pancreatic extracellular volume fraction analysis using contrast-enhanced CT in patients with diabetes mellitus and pre-diabetes
PurposeLiver and pancreatic fibrosis is associated with diabetes mellitus (DM), and liver fibrosis is associated with pancreatic fibrosis. This study...
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Assessment of hepatic fat content and prediction of myocardial fibrosis in athletes by using proton density fat fraction sequence
PurposeTo explore the characteristics of the hepatic fat content in athletes, and predict late gadolinium enhancement (LGE) based on magnetic...
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Primary hepatic myopericytoma coexisting with multiple cystic hepatic lesions: a case report
BackgroundHepatic myopericytoma (MPC) is an extremely rare pathological entity in the liver. Conversely, cystic hepatic lesions are a group of...
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Comparative study between liver biopsy and non-invasive biomarkers in assessment of hepatic fibrosis in children with chronic liver diseases
BackgroundLiver biopsy is the gold standard for detecting the degree of liver fibrosis; however, invasiveness constitutes its main limiting factor in...
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Clinical study of the value of shear wave elastography in evaluating the degree of liver fibrosis in children
ObjectivesTo explore the clinical application of shear wave elastography (SWE) in evaluating the degree of liver fibrosis in children.
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Laterality of CT-measured hepatic extracellular volume fraction in patients with chronic thromboembolic pulmonary hypertension
PurposeThis study examines the hepatic extracellular volume fraction (ECV) disparity between the left and right lobes (ECV_left and ECV_right) in...
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Postnatal treatment and evolution patterns of giant fetal hepatic hemangioma: a case series of 29 patients
ObjectivesTo explore the clinical characteristics, postnatal treatment and prognosis of giant fetal hepatic hemangioma (GFHH).
Method ...
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Novel Approaches to the Failing Congenital Heart
Purpose of ReviewHeart failure is the leading cause of morbidity and mortality in adults with congenital heart disease and is characterized by a...
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Low skeletal muscle mass and liver fibrosis in children with cerebral palsy
The purpose of the study was to conduct a nutritional and metabolic assessment of children with cerebral palsy, including an investigation of liver...
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Hepatic manifestations of systemic disease: an imaging-based review
The liver is responsible for many processes that maintain human metabolic homeostasis and can be affected by several pediatric systemic diseases. In...
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Significantly elevated hepatic extracellular volume in adult patients with a Fontan circulation and its correlation with impaired functional capacity
Fontan-associated liver disease is a major concern in patients who have undergone the procedure. Regular imaging of the liver is currently...
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The Right Heart in Congenital Heart Disease
Purpose of ReviewTo analyze the pathophysiologic importance of the right heart in different types of congenital heart disease (CHD), summarize...
