15 Result(s)
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Mohammad Hadi Imanieh
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Article
Open AccessIdentification of two Iranian siblings with cerebrotendinous xanthomatosis: a case report
Cerebrotendinous xanthomatosis (CTX) is a rare autosomal recessive lipid storage disorder that leads to multisystem involvement. It is caused by mutations in the CYP27A1 gene which encodes the mitochondrial enzym...
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Open AccessManifestation of leech infestation as severe gastrointestinal bleeding in a 3-year-old boy: a case report and review of the literature
Leeches are a class of hermaphroditic parasites that can attach to various body parts and start sucking blood. Gastrointestinal (GI) bleeding due to leeches is a rare phenomenon that is more common in less dev...
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Open AccessAn evaluation of ascitic calprotectin for diagnosis of ascitic fluid infection in children with cirrhosis
The most common infection in children with the hepatic disease with or without cirrhotic ascites is spontaneous bacterial peritonitis (SBP), which occurs in the absence of an evident intra-abdominal source of ...
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Open AccessAuthor Correction: Clinical and genetic spectrum of glycogen storage disease in Iranian population using targeted gene sequencing
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Open AccessPediatric liver and kidney transplantation in the era of COVID-19: a follow-up study from a tertiary referral center in Iran
We aimed to evaluate the impact of COVID-19 pandemic on pediatric transplant outcomes and determine whether to continue pediatric transplant activity or not, and how policies intended our center has been effec...
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Open AccessClinical and genetic spectrum of glycogen storage disease in Iranian population using targeted gene sequencing
Glycogen storage diseases (GSDs) are known as complex disorders with overlap** manifestations. These features also preclude a specific clinical diagnosis, requiring more accurate paraclinical tests. To evalu...
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Open AccessRosai-Dorfman disease: a rare presentation with para-aortic and mesenteric lymphadenopathy, hepatosplenomegaly and ascites
Rosai-Dorfman disease (RDD) is a rare but well-defined, histiocytic proliferative disorder with massive lymphadenopathy.
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Article
Lessons from one year experience of pooled procurement of pharmaceuticals: exploration of indicators and assessing pharmacies` performance
Joint procurement of medicines is a way to improve access and justice in develo** countries. The aim of this study is to determine local indicators for assessing the performance of joint procurement agencies...
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Aspartate aminotransferase to platelet ratio index and severity of hepatic fibrosis in children
Liver biopsy is the gold standard for detection of the severity of liver fibrosis and cirrhosis. However, it is limited by invasiveness, complications, sampling error, and variability in pathological interpret...
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Article
The healing effect of Curcuma longa on liver in experimental acute hepatic encephalopathy of rat
Hepatic encephalopathy (HE) is a potentially reversible spectral neuropsychiatric state that complicates liver disease and negatively affects the prognosis. This study evaluated the effect of Curcuma longa in acu...
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A new mutation of Fanconi–Bickel syndrome with liver failure and pseudotumour cerebri
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Article
Triangular Cord Sign in Detection of Biliary Atresia: Is It a Valuable Sign?
Background Early detection of biliary atresia (BA) has a vital role in prevention of liver cirrhosis in these patients. There are some evidences that triangular cord (TC) sign, i.e., tria...
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Efficacy of the Standard Quadruple Therapy Versus Triple Therapies Containing Proton Pump Inhibitor Plus Amoxicillin and Clarithromycin or Amoxicillin-Clavulanic Acid and Metronidazole for Helicobacter pylori Eradication in Children
ObjectivesHelicobacter pylori (H. pylori) cure rates vary in different geographical regions because of differences in hosts as well as in H. pylori strains. In this study we evaluated the efficacy of different tr...
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Upper gastrointestinal bleeding in children in Southern Iran
To find out whether the causes of upper GI bleeding in our center in a develo** country differed from developed countries.
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Hyperlipidemia in Iranian liver transplant recipients: prevalence and risk factors
Hyperlipidemia is a metabolic complication after liver transplantation (LT). The aim of this study was to investigate the prevalence and risk factors for develo** hyperlipidemia in patients who underwent LT ...
