![Loading...](https://link.springer.com/static/c4a417b97a76cc2980e3c25e2271af3129e08bbe/images/pdf-preview/spacer.gif)
-
Article
A Novel CEBPE Variant Causes Severe Infections and Profound Neutropenia
Specific granule deficiency (SGD) is a rare inborn error of immunity resulting from loss-of-function variants in CEBPE gene (encoding for transcription factor C/EBPε). Although this genetic etiology has been know...
-
Article
Tolvaptan therapy for massive edema in a patient with nephrotic syndrome
Nephrotic syndrome (NS) is characterized by water and sodium retention, which leads to edema. The non-osmotic stimulation of arginine vasopressin release from the pituitary gland has been implicated as one of ...
-
Article
Formation of a pseudorotaxane, capable of sensing cations via dethreading molecular motion, from a cryptand and bipyridinium salts
A new type of cryptand-based pseudorotaxane was prepared, utilizing a novel cryptand incorporating two aromatic rings as a wheel component, combined with various bipyridinium salts as the axle component. These...
-
Article
Rapid Detection of Intracellular p47phox and p67phox by Flow Cytometry; Useful Screening Tests for Chronic Granulomatous Disease
Chronic granulomatous disease (CGD) is caused by defects of NADPH oxidase. The diagnosis of CGD can be made by analysis of NADPH oxidase activity, however, identification of the CGD subgroups is required befor...
-
Article
Characterization of stable, electroactive protein cage/synthetic polymer multilayer thin films prepared by layer-by-layer assembly
We have fabricated electroactive multilayer thin films containing ferritin protein cages. The multilayer thin films were prepared on a solid substrate by the alternate electrostatic adsorption of (apo)ferritin...
-
Article
Fabrication of Semiconductor Nano-particles in the Protein Cage of Apoferritin
We specially designed a slow chemical reaction system to synthesize the zinc selenide nanoparticles (ZnSe NPs), in the cavity of the cage-shaped protein, apoferritin. The newly designed chemical synthesis syst...
-
Article
Catalytic hydrogenation of linoleic acid over platinum-group metals supported on alumina
Catalytic activity and selectivity for hydrogenation of linoleic acid (cis-9,cis-12 18:2) were studied on Pt, Pd, Ru, and Ir supported on Al2O3. Stearic acid (18:0) and 10 different octadecenoic isomers (18:1) in...
-
Article
Catalytic hydrogenation of linoleic acid on nickel, copper, and palladium
The catalytic activity and selectivity for hydrogenation of linoleic acid were studied on Ni, Cu, and Pd catalysts. A detailed analysis of the reaction product was performed by a gas-liquid chromatograph, equi...