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Article
The relation of the multifocal electroretinographic response to macular layer volume
To determine the association of the multifocal electroretinographic (mfERG) response amplitude with the volumes of the inner, postreceptor, and photoreceptor retinal layers in the region stimulated by each mfERG ...
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Reference Work Entry In depth
Visual Impairment in Infants and Young Children
Visual impairment in pediatric patients is caused by disorders within the eye or in the brain. No matter the cause, measurement of visual function and comparison to normal values for age contributes to the dia...
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Article
Dark-adapted threshold and electroretinogram for diagnosis of Usher syndrome
To determine the utility of ophthalmology evaluation, dark-adapted threshold, and full-field electroretinogram for early detection of Usher syndrome in young patients with bilateral sensorineural hearing loss.
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Article
Open AccessBroadening INPP5E phenotypic spectrum: detection of rare variants in syndromic and non-syndromic IRD
Pathogenic variants in INPP5E cause Joubert syndrome (JBTS), a ciliopathy with retinal involvement. However, despite sporadic cases in large cohort sequencing studies, a clear association with non-syndromic inher...
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Living Reference Work Entry In depth
Visual Impairment in Infants and Young Children
Visual impairment in pediatric patients is caused by disorders within the eye or in the brain. No matter the cause, measurement of visual function and comparison to normal values for age contributes to the dia...
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Article
Open AccessISCEV guide to visual electrodiagnostic procedures
Clinical electrophysiological testing of the visual system incorporates a range of noninvasive tests and provides an objective indication of function relating to different locations and cell types within the v...
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Article
Progressive retinal degeneration in a girl with Knobloch syndrome who presented with signs of ocular albinism
We report for the first time electroretinographic (ERG) evidence of progressive retinal abnormalities in a girl who presented in infancy with ocular features of albinism and gradually developed choroidal scler...
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Article
Differentiation of murine models of “negative ERG” by single and repetitive light stimuli
Marked attenuation of the single-flash electroretinographic (ERG) b-wave in the presence of a normal-amplitude or less-attenuated a-wave is commonly referred to as the “negative ERG.” The purpose of this study...
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Article
Vigabatrin can enhance electroretinographic responses in pigmented and albino rats
To evaluate the effects of the antiepileptic medication vigabatrin (VGB) on the retina of pigmented rats.
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Article
Introduction to the special issue: Vision after Premature Birth
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Article
Alterations of the tunica vasculosa lentis in the rat model of retinopathy of prematurity
To study the relationship between retinal and tunica vasculosa lentis (TVL) disease in retinopathy of prematurity (ROP). Although the clinical hallmark of ROP is abnormal retinal blood vessels, the vessels of ...
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Article
Next-generation sequencing analysis of gene regulation in the rat model of retinopathy of prematurity
The purpose of this study was to identify the genes, biochemical signaling pathways, and biological themes involved in the pathogenesis of retinopathy of prematurity (ROP).
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Article
Electroretinographic (ERG) responses in pediatric patients using vigabatrin
The antiepileptic drug vigabatrin is known to cause retinal and visual dysfunction, particularly visual field defects, in some patients. Electroretinography (ERG) is used in an attempt to identify adverse effe...
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Article
Long-term effects of retinopathy of prematurity (ROP) on rod and rod-driven function
The purpose of this study was to determine whether recovery of scotopic sensitivity occurs in human ROP, as it does in the rat models of ROP. Following a cross-sectional design, scotopic electroretinographic (...
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Article
Cone ERG responses in patients with Smith-Lemli-Opitz Syndrome (SLOS)
To evaluate cone and cone-driven retinal function in patients with Smith-Lemli-Opitz syndrome (SLOS), a condition characterized by low cholesterol. Rod and rod-driven function in patients with SLOS are known t...
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Article
Deactivation of the rod response in retinopathy of prematurity
It is known that retinopathy of prematurity (ROP) alters the activation of rod photoreceptors, but the effect of ROP on deactivation has not been investigated. We studied deactivation using an electroretinogra...
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Article
The anatomy of the rat eye with oxygen-induced retinopathy
Prior studies have documented the intertwined developmental courses of retinal blood vessel tortuosity (in fundus photographs) and retinal dysfunction (in electroretinographs) in Sprague–Dawley rat models of r...
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Article
Retinal degenerative and hypoxic ischemic disease
A broad spectrum of retinal diseases affects both the retinal vasculature and the neural retina, including photoreceptor and postreceptor layers. The accepted clinical hallmarks of acute retinopathy of prematu...
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Article
Pediatric clinical visual electrophysiology: a survey of actual practice
Survey the actual clinical practice of pediatric visual electrophysiology. The electrophysiologists surveyed were members of the International Society for Clinical Electrophysiology of Vision (ISCEV).
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Article
Multifocal ERG in Subjects with a History of Retinopathy of Prematurity
Purpose: Investigate the function of the central retina in subjects with a history of retinopathy of prematurity (ROP). Methods: Multifocal electroretinogram (mfERG) responses to a scaled array of 103 hexagons we...
