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Cochlear Implant in cochlear Hypoplasia type 4 with Chiari Malformation- Case Report

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Abstract

Cochlear hypoplasia type IV is a rare cochlear malformation with hypoplastic middle and apical turns while basal turn develops normally, it often coexist with other genetic mutations. We present a case of 4 year old with chiari malformation type 1 along with bilateral Cochlear hypoplasia type IV who underwent cochlear implantation.

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Correspondence to Neeraj Suri.

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Suri, N., Singh, A. & Sharma, D. Cochlear Implant in cochlear Hypoplasia type 4 with Chiari Malformation- Case Report. Indian J Otolaryngol Head Neck Surg 75, 2467–2469 (2023). https://doi.org/10.1007/s12070-023-03757-7

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