Abstract
Cochlear hypoplasia (CH) represents a group of inner ear malformations in which dimensions are less than those of a normal cochlea with various internal architecture deformities. In cochlear hypoplasia, there is a clear differentiation between cochlea and vestibule. Four different types of cochlear hypoplasia can be identified. Types of hearing loss range from conductive, mixed to sensorineural hearing loss, while degree of hearing loss shows variation from moderate to profound. Most common presentation is profound sensorineural hearing loss. Gusher and meningitis may be encountered in CH-II. CH is the group where facial nerve abnormality is most commonly encountered. Frequent stapes fixation or oval window atresia makes stapedotomy a treatment option. According to the presence of cochlear nerve, cochlear or brainstem implantation may be indicated. In this chapter, radiological, audiological features, and surgical considerations of cochlear hypoplasia along with case presentations are provided.
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Sennaroglu, L., Cinar, B.C., Ozgen, B., Pamuk, G. (2022). Cochlear Hypoplasia. In: Sennaroglu, L. (eds) Inner Ear Malformations. Springer, Cham. https://doi.org/10.1007/978-3-030-83674-0_26
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DOI: https://doi.org/10.1007/978-3-030-83674-0_26
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