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S100-negative epithelioid malignant peripheral nerve sheath tumor with possible perineurial differentiation
Epithelioid malignant peripheral nerve sheath tumor (MPNST) is a rare subtype of MPNST composed of epithelioid cells with abundant cytoplasm....
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A case report on a novel use of intraoperative Intrabeam™ radiation therapy for a recurrent malignant peripheral nerve sheath tumor with sciatic nerve involvement
BackgroundMalignant peripheral nerve sheath tumors (MPNST) are sarcomas that arise from peripheral nerves. They generally have a poor prognosis which...
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Delayed emergence from anesthesia caused by an intraoperative cerebral embolism of a malignant peripheral nerve sheath tumor in a neurofibromatosis type 1 patient: a case report
BackgroundMalignant peripheral nerve sheath tumors (MPNSTs) are aggressive soft tissue sarcomas which commonly arise from neurofibromatosis type 1....
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Malignant peripheral nerve sheath tumor (MPNST) and MPNST-like entities are defined by a specific DNA methylation profile in pediatric and juvenile population
BackgroundMalignant peripheral nerve sheath tumors (MPNSTs) account for 3–10% of pediatric sarcomas, 50% of which occur in neurofibromatosis type 1...
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Reconstruction of a pediatric malignant peripheral nerve sheath tumor with a free osteocutaneous fibula flap: a case report
Malignant peripheral nerve sheath tumor (MPNST) is an extremely rare and biologically aggressive tumor. Treatment should ensure wide resection with...
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Survival outcomes of malignant peripheral nerve sheath tumors (MPNSTs) with and without neurofibromatosis type I (NF1): a meta-analysis
IntroductionMalignant peripheral nerve sheath tumors (MPNSTs) are malignancies that demonstrate nerve sheath differentiation in the peripheral...
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Benign peripheral nerve sheath tumors: an interdisciplinary diagnostic and therapeutic challenge
A benign peripheral nerve sheath tumor (bPNST) is a rare lesion associated with peripheral nerval structures. Symptoms may be heterogeneous,...
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Experimental models of undifferentiated pleomorphic sarcoma and malignant peripheral nerve sheath tumor
Undifferentiated pleomorphic sarcoma (UPS) and malignant peripheral nerve sheath tumor (MPNST) are aggressive soft tissue sarcomas that do not...
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Brachial plexus peripheral nerve sheath tumors (PNSTs): clinical and surgical management in the pediatric population
PurposePeripheral nerve sheath tumors (PNSTs) are rare in pediatric patients, especially in the brachial plexus. Research on PNSTs is lacking. This...
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The role of radiotherapy in the management of malignant peripheral nerve sheath tumors: a single-center retrospective cohort study
PurposeThis study sought to investigate the role of radiotherapy (RT) in addition to surgery for oncological outcomes in patients with malignant...
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Peripheral Nerve Sheath Tumors of the Orbit
Peripheral nerve sheath tumors (PNSTs) are neoplasms that arise from peripheral nerves or demonstrate nerve sheath differentiation. They usually...
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Malignant Peripheral Nerve Sheath Tumor Arising from Small Bowel Mesentery: an Extremely Rare Case with Review of Literature
PurposeMalignant peripheral nerve sheath tumor (MPNST) of small bowel mesentery is a rare tumor. We report a rare case of MPNST of small bowel...
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Other Nerve Sheath Tumors of Brain and Spinal Cord
The three main types of nerve sheath tumors are schwannomas, neurofibromasNeurofibroma and perineuriomasPerineurioma. Multiple neurofibromas...
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Circulating tumor DNA for malignant peripheral nerve sheath tumors in neurofibromatosis type 1
PurposeThe leading cause of early death in patients with neurofibromatosis type 1 (NF1) is malignant peripheral nerve sheath tumor (MPNST). The...
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Recurrent malignant peripheral nerve sheath tumor presenting as an asymptomatic intravenous thrombus extending to the heart: a case report
BackgroundMalignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue sarcoma mainly treated via surgical resection. Herein, we report a...
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Malignant Peripheral Nerve Sheath Tumors
Several types of malignant tumors may affect peripheral nerves, among whom the malignant peripheral nerve sheath tumors (MPNST) are the most common....
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A para-aortic malignant melanotic nerve sheath tumor mimicking a gastrointestinal stromal tumor: a rare case report and review of literature
BackgroundMalignant melanotic nerve sheath tumor (MMNST), formerly called melanotic schwannoma, is a rare tumor of neural crest derivation which most...
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Markers and Immunoprofile of Peripheral Nerve and Nerve Sheath Tumors
S100, CD56, PGP 9.5, Sox-10, Myelin basic protein, Glial fibrillary acidic protein (GFAP), Neurofilaments, Nerve growth factor receptor (NGFR, gp75),...
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Giant Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Treated with Multiorgan Resection: a Case Report and Review of the Literature
Malignant peripheral nerve sheath tumors (MPNST) are rare. Although they originate from Schwann cells or pluripotent neural crest cells, they...
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Malignant nerve sheath tumor of oculomotor nerve in a pediatric patient
Malignant nerve sheath tumors are extremely rare pathologies. They tend to occur within peripheral nerves and have close association of...
