Search
Search Results
-
Primary bilateral macronodular adrenal hyperplasia: definitely a genetic disease
Primary bilateral macronodular adrenal hyperplasia (PBMAH) is an adrenal cause of Cushing syndrome. Nowadays, a PBMAH diagnosis is more frequent than...
-
The effect of unilateral adrenalectomy on patients with primary bilateral macronodular adrenal hyperplasia
PurposeTo evaluate the long-term effect of unilateral adrenalectomy (uADX) on patients with primary bilateral macronodular adrenal hyperplasia...
-
Corticotropin-releasing hormone test predicts the outcome of unilateral adrenalectomy in primary bilateral macronodular adrenal hyperplasia
PurposePrimary bilateral adrenal hyperplasia (PBMAH) is associated with hypercortisolism and a heterogeneous clinical expression in terms of cortisol...
-
Primary bilateral macronodular adrenocortical hyperplasia (PBMAH) patient with ARMC5 mutations
BackgroundPrimary bilateral macronodular adrenocortical hyperplasia (PBMAH) is a highly heterogeneous disease with divergent manifestations ranging...
-
A novel pathogenic variant of ARMC5 in a patient with primary bilateral macronodular adrenal hyperplasia: a case report
BackgroundPrimary bilateral macronodular adrenal hyperplasia (PBMAH), also known as adrenocorticotropic hormone (ACTH)-independent macronodular...
-
The role of adrenal venous sampling (AVS) in primary bilateral macronodular adrenocortical hyperplasia (PBMAH): a study of 16 patients
ObjectivePrimary bilateral macronodular adrenocortical hyperplasia (PBMAH) is a rare cause of ACTH-independent Cushing’s syndrome. Current guidelines...
-
Update on primary bilateral macronodular adrenal hyperplasia (PBMAH)
Primary bilateral macronodular adrenal hyperplasia (PBMAH), characterized by bilateral benign adrenal macronodules (>1 cm) potentially responsible...
-
MicroRNA expression signature and target prediction in familial and sporadic primary macronodular adrenal hyperplasia (PMAH)
BackgroundPrimary macronodular adrenal hyperplasia (PMAH), previously termed ACTH-independent macronodular adrenal hyperplasia (AIMAH), is a rare...
-
Unilateral adrenalectomy partially improved hyperglycemia in a patient with primary bilateral macronodular adrenal hyperplasia
Primary bilateral macronodular adrenal hyperplasia (PBMAH) is characterized by bilateral multiple adrenal macro-nodules that often cause mild...
-
Uncommon adrenal rest tumors and massive adrenal enlargement in adult with congenital adrenal hyperplasia mimicking metastasis from pleomorphic sarcoma
BackgroundCongenital adrenal hyperplasia (CAH) encompassed a bunch of autosomal recessive disorders characterized by impaired cortisol levels due to...
-
Clinical analysis of the etiological spectrum of bilateral adrenal lesions: A large retrospective, single-center study
PurposeTo investigate the clinical characteristics, endocrinological function, and etiology of bilateral adrenal lesions in hospitalized patients.
...
-
Morphological Harbingers of ARMC5-Pathogenic Variant-Related Bilateral Macronodular Adrenocortical Disease
Bilateral macronodular adrenocortical disease (BMAD) is a neoplastic disease associated with a high frequency of germline disease. Armadillo repeat...
-
Primary adrenal diffuse large B cell Lymphoma with Tumor thrombus in central adrenal vein: a case report and literature review
BackgroundPrimary adrenal lymphoma (PAL) is a rare disease confined wholly or chiefly to extramural involvement. Tumor thrombus in the central...
-
Role of adrenal venous sampling in the differential diagnosis and treatment protocol of ACTH-independent Cushing’s syndrome with bilateral adrenal lesions
PurposeThe diagnosis and management of adrenocorticotropic hormone-independent Cushing’s syndrome (AICS) with bilateral adrenal lesions remain...
-
Severe osteoporosis in a young man with bilateral Cushing’s syndrome: a case report
BackgroundThe diagnosis of Cushing’s syndrome is challenging; however, through the clinical picture and the search for secondary causes of...
-
Impact of Morphology in the Genotype and Phenotype Correlation of Bilateral Macronodular Adrenocortical Disease (BMAD): A Series of Clinicopathologically Well-Characterized 35 Cases
Bilateral macronodular adrenocortical disease (BMAD) is characterized by the development of adrenal macronodules resulting in a pituitary-ACTH...
-
Unilateral Adrenalectomy for Primary Aldosteronism Due to Bilateral Adrenal Disease Can Result in Resolution of Hypokalemia and Amelioration of Hypertension
BackgroundBilateral idiopathic hyperaldosteronism (IHA) is responsible for 60% of primary aldosteronism (PA) cases. Medical management is standard of...
-
Neuroradiological features of patients with bilateral macronodular adrenocortical disease and meningiomas associated or not with genetic variants of ARMC5– a case series
IntroductionMeningiomas are the most common primary brain and central nervous system tumors, accounting for approximately 40% of these tumors. The...
-
Overview of the 2022 WHO Classification of Adrenal Cortical Tumors
The new WHO classification of adrenal cortical proliferations reflects translational advances in the fields of endocrine pathology, oncology and...
-
High prevalence of adrenal cortical adenomas in patients with cerebral meningiomas
PurposeAdrenal cortical adenomas (ACAs) represent one of the most common endocrine neoplasms. Recently, a genetic syndrome, characterized by...