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Fractional exhaled nitric oxide in idiopathic pulmonary arterial hypertension and mixed connective tissue disease complicating pulmonary hypertension
BackgroundFractional exhaled nitric oxide (FeNO) has been extensively studied in various causes of pulmonary hypertension (PH), but its utility as a...
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Role and predictive value of microRNAs 204 and 210 in the diagnosis of pulmonary arterial hypertension and the distinction between idiopathic, systemic sclerosis, and schistosomiasis-associated pulmonary arterial hypertension
BackgroundPulmonary arterial hypertension is most of the time diagnosed late in the course of the disease and necessitates right cardiac...
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ECMO Bridge to Lung Transplant in Children with Idiopathic Pulmonary Arterial Hypertension
Idiopathic pulmonary arterial hypertension (IPAH) represents an important clinical indication for lung transplant (LTx) in children. Recent trends...
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Serum PM20D1 levels in patients with idiopathic pulmonary arterial hypertension and its clinical significance
ObjectiveThis study aimed to investigate the serum levels of Peptidase M20 domain containing 1 (PM20D1) in idiopathic pulmonary arterial hypertension...
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Predicting Peri-Operative Cardiorespiratory Adverse Events in Children with Idiopathic Pulmonary Arterial Hypertension Undergoing Cardiac Catheterization Using Echocardiography: A Cohort Study
General anesthesia in children with idiopathic pulmonary arterial hypertension (PAH) carries an increased risk of peri-operative cardiorespiratory...
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Impact of diabetes mellitus on disease severity and patient survival in idiopathic pulmonary arterial hypertension: data from the Polish multicentre registry (BNP-PL)
BackgroundRecent studies revealed that alterations in glucose and lipid metabolism in idiopathic pulmonary arterial hypertension (IPAH) are...
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Novel Drugs for the Treatment of Pulmonary Arterial Hypertension: Where Are We Going?
Pulmonary arterial hypertension (PAH) is a progressive disease that despite advances in therapy is associated with a 7-year survival of approximately...
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Artificial intelligence-based model for predicting pulmonary arterial hypertension on chest x-ray images
BackgroundPulmonary arterial hypertension is a serious medical condition. However, the condition is often misdiagnosed or a rather long delay occurs...
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Coexistence of pulmonary arterial hypertension and straight back syndrome in a patient with a novel BMPR2 variant affecting cytoplasmic tail domain
BackgroundPathologic variants in the bone morphogenetic protein receptor-2 ( BMPR2 ) gene cause a pulmonary arterial hypertension phenotype in an...
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Association of non-insulin-based insulin resistance indices with disease severity and adverse outcome in idiopathic pulmonary arterial hypertension: a multi-center cohort study
BackgroundInsulin resistance (IR) plays an important role in the pathophysiology of cardiovascular disease. Recent studies have shown that diabetes...
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Severe Pulmonary Arterial Hypertension in Healthy Young Infants: Single Center Experience
ObjectivesWe studied the clinical presentation and management of acute pulmonary arterial hypertension (PAH) in healthy young infants, and the effect...
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Future Perspectives of Pulmonary Arterial Hypertension: A Review of Novel Pipeline Treatments and Indications
Pulmonary arterial hypertension is characterized by elevated blood pressure and pathological changes in the pulmonary arterioles, leading to the...
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A PrOsPective Cohort Study on Interstitial Lung Disease-Associated Pulmonary Hypertension with a ParticulaR Focus on the Subset with Pulmonary Arterial Hypertension Features (POPLAR Study)
IntroductionThe pathogenesis and clinical profiles of patients with pulmonary hypertension (PH) associated with interstitial lung disease (ILD-PH)...
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Advances in targeted therapy for pulmonary arterial hypertension in children
Pulmonary arterial hypertension (PAH) is a rare and devastating disease of the pulmonary vasculature with a high morbidity and mortality rate in...
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Resistin predicts disease severity and survival in patients with pulmonary arterial hypertension
BackgroundAbnormal remodeling of distal pulmonary arteries in patients with pulmonary arterial hypertension (PAH) leads to progressively increased...
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Pulmonary hypertension
Pulmonary hypertension encompasses a range of conditions directly or indirectly leading to elevated pressures within the pulmonary arteries. Five...
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Prostaglandin and prostaglandin receptors: present and future promising therapeutic targets for pulmonary arterial hypertension
BackgroundPulmonary arterial hypertension (PAH), Group 1 pulmonary hypertension (PH), is a type of pulmonary vascular disease characterized by...
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Charting the cellular landscape of pulmonary arterial hypertension through single-cell omics
This review examines how single-cell omics technologies, particularly single-cell RNA sequencing (scRNAseq), enhance our understanding of pulmonary...
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Medical Management of Right Ventricular Dysfunction in Pulmonary Arterial Hypertension
Purpose of ReviewThe purpose of this review is to overview the most relevant and recent knowledge regarding medical management in pulmonary arterial...
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Real-World Management of Patients with Pulmonary Arterial Hypertension: Insights from EXPOSURE
IntroductionFurther insights into real-world management and outcomes of patients with pulmonary arterial hypertension (PAH) are needed. This interim...
