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Article
67 USE OF POCKET COMPUTER BY PATIENTS WITH METABOLIC DISORDERS TO ADJUST THEIR DAILY NUTRITIONAL INTAKE
After 5 years of age, one of the major problems to continue a special diet by patient with metabolic disorders is the anorexia. A likely cause is an imbalance due to the scarcity of choice in foodstuff availab...
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Article
90 PLASMA FATTY ACIDS IN PARENTERALLY FED PREMATURE AND TERM BORN INFRANTS: CHANGES INDUCED BY INTRALIPID AND SUNFLOWER-SEED OIL
Premature infants receiving PN free of fat soon develop essential fatty acid (EFA) deficiency, whereas they often have less than 1% of their body weight as fatdeposit. Experience has shown that Intralipid (IL)...
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Article
Liver Peroxisome Damage during Acute Hepatic Failure in Partial Ornithine Transcarbamylase Deficiency
Summary: A boy with ornithine transcarbamylase (OTC) deficiency was relatively symptom free for 9 months and then developed an acute episode with liver failure and metabolic imbalance. Subsequently there was s...