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The Adult with Tetralogy of Fallot

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Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care

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Abstract

The tetralogy of Fallot (TOF) is the most common form of cyanotic congenital heart disease.

Few are, today, the patients with TOF that reach the adulthood in natural history. Innovations in the diagnosis and management of TOF have led to dramatic improvements in early survival. As a result, the population of TOF repair survivors is growing rapidly. Surgical management of TOF leaves anatomic and functional abnormalities in the majority of patients. We will discuss in this chapter the different issues related to the most important problems (as chronic pulmonary valve insufficiency and obstruction of the right ventricular outflow tract, right ventricular outflow tract aneurism, pulmonary branch artery stenosis, dilated ascending aorta, aortic regurgitation, residual ventricular septal defect, arrhythmic problems) that we can face during the daily clinical practice, managing these patients.

We will conclude discussing some important aspects of the post-op management of the right ventricular function.

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Author information

Authors and Affiliations

  1. Cardio-Thoracic Anesthesia and ICU, IRCCS- Policlinico San Donato, San Donato Milanese, Italy

    Giuseppe Isgrò & Marco Ranucci

  2. Cardio-Thoracic Surgery, IRCCS- Policlinico San Donato, San Donato Milanese, Italy

    Alessandro Giamberti

  3. Arrhythmia and Electrophysiology Center, IRCCS- Policlinico San Donato, San Donato Milanese, Italy

    Sara Foresti

  4. Pediatric and Adult Congenital Heart Center, IRCCS- Policlinico San Donato, San Donato Milanese, Italy

    Massimo Chessa

Authors
  1. Giuseppe Isgrò
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  2. Alessandro Giamberti
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  3. Marco Ranucci
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  4. Sara Foresti
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  5. Massimo Chessa
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Editor information

Editors and Affiliations

  1. Children’s Hospital Colorado University of Colorado Denver, School of, Aurora, CO, USA

    Eduardo M. da Cruz

  2. Children's Hospital Colorado University of Colorado School of Medicin, Aurora, CO, USA

    Dunbar Ivy

  3. Department of Cardiac Surgery, German Pediatric Heart Center, Sankt Augustin, Germany

    Viktor Hraska

  4. Pediatric Cardiac Surgery, Children's Hospital Colorado University of Colorado, Aurora, CO, USA

    James Jaggers

Section Editor information

  1. Cincinnati Children’s Hospital Medical Center, Cincinatti, OH, USA

    Gary Webb

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Isgrò, G., Giamberti, A., Ranucci, M., Foresti, S., Chessa, M. (2023). The Adult with Tetralogy of Fallot. In: da Cruz, E.M., Ivy, D., Hraska, V., Jaggers, J. (eds) Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care. Springer, London. https://doi.org/10.1007/978-1-4471-4999-6_185-2

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  • DOI: https://doi.org/10.1007/978-1-4471-4999-6_185-2

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