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Intestinal duplications — intestinal diverticula — segmental dilatation of the intestine: a common genetic complex

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Abstract

The rare disorder, segmental dilatation of the intestine (SDI), leads to functional obstruction without stenosis and with normally functioning ganglion cells. No theory as to the pathogenesis of this congenital malformation has been proposed as yet. We hypothesize that SDI is caused by a disturbance during splitting of the notochord from the entoderm as a part of a common complex consisting of SDI, congenital diverticula, and intestinal duplications.

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Authors and Affiliations

  1. Department of Surgery, Section of Pediatric Surgery, J. W. Goethe University Frankfurt, Theodor-Stern-Kai 7, D-6000, Frankfurt am Main 70, Federal Republic of Germany

    K. Heller, K. -L. Waag & F. Beyersdorf

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  1. K. Heller
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  2. K. -L. Waag
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  3. F. Beyersdorf
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Heller, K., Waag, K.L. & Beyersdorf, F. Intestinal duplications — intestinal diverticula — segmental dilatation of the intestine: a common genetic complex. Pediatr Surg Int 4, 249–253 (1989). https://doi.org/10.1007/BF00177493

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