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Substitutionstherapie mit hochgereinigtem Protein C-Konzentrat bei einem Kind mit homozygotem Protein C-Mangel

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17. Hämophilie-Symposion

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Zusammenfassung

Ein 11 Monate altes arabisches Mädchen, 6. Kind blutsverwandter Eltern, kam zur stationären Aufnahme. Im 7. Lebensmonat fielen erstmals rezidivierende Ekchymo-sen auf, im 9. Lebensmonat dann eine 10 × 10 cm große Hautnekrose an der linken Flanke. Das Kind wurde zunächst in die Universitätsklinik Charlottenburg in Berlin, dann in unsere Klinik verlegt. Unabhängig voneinander wurde die Diagnose „homozygoter Protein C-Mangel“ gestellt.

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Author information

Authors and Affiliations

  1. München, Deutschland

    K. Auberger, H. Engelmann, J. Weil, Ch. Brückmann, B. Dietz, W. Schramm, Th. Vukovich & H. B. Hadorn

  2. Wien, Österreich

    K. Auberger, H. Engelmann, J. Weil, Ch. Brückmann, B. Dietz, W. Schramm, Th. Vukovich & H. B. Hadorn

Authors
  1. K. Auberger
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  2. H. Engelmann
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  3. J. Weil
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  4. Ch. Brückmann
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  5. B. Dietz
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  6. W. Schramm
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  7. Th. Vukovich
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  8. H. B. Hadorn
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Editor information

Editors and Affiliations

  1. Abteilung Hämatologie und Onkologie, Universität-Kinderklinik, Martinistraße 52, 2000, Hamburg 20, Deutschland

    G. Landbeck

  2. 8000, München, Deutschland

    R. Marx

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© 1988 Springer-Verlag Berlin Heidelberg

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Auberger, K. et al. (1988). Substitutionstherapie mit hochgereinigtem Protein C-Konzentrat bei einem Kind mit homozygotem Protein C-Mangel. In: Landbeck, G., Marx, R. (eds) 17. Hämophilie-Symposion. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-72830-3_85

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  • DOI: https://doi.org/10.1007/978-3-642-72830-3_85

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-18065-4

  • Online ISBN: 978-3-642-72830-3

  • eBook Packages: Springer Book Archive

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