Zusammenfassung
Die zystische Fibrose bzw. Mukoviszidose ist die häufigste Erbkrankheit weltweit. Ihre Inzidenz in Deutschland liegt bei ca. 1 pro 2.500 Lebendgeburten. Die geschätzte Zahl an Mukoviszidosepatienten in Deutschland beträgt 7.000; davon sind 2.284 in einem zentralen, nationalen Register erfaßt (Qualitätssicherung Mukoviszidose 1996).
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Teschendorf, C., Schmiegel, W. (2000). Zystische Fibrose. In: Adler, G., Beglinger, C., Manns, M.P., Müller-Lissner, S., Schmiegel, W. (eds) Klinische Gastroenterologie und Stoffwechsel. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-57194-7_70
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