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(Neo) Vaginoplasty in Female Pelvic Congenital Anomalies

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Female Genitourinary and Pelvic Floor Reconstruction

Abstract

Congenital pelvic malformations are rare conditions characterized by specific common features resulting from an abnormal embryological development of the urogenital and anorectal apparatus. Anomalies in pelvic morphology caused by these malformations lead to complex management and surgical planning. Vaginal absence or hypoplasia is commonly found in females with these conditions. Vaginoplasty and neovaginoplasty are the surgical mainstays for functional, aesthetic, and reproductive restoration in these cases. These procedures aim to achieve an adequately sized and located vagina, as well as normal appearing external female genitalia.

A variety of vaginoplasty techniques exist with similar outcomes. Surgeon experience, complexity of vaginal defects and convergence between the vagina and the urethra are factors that impact surgical decision-making.

Management of congenital pelvic malformations in the context of disorders of sexual differentiation is often complex and sometimes controversial, and must be undertaken by trained specialists including a multidisciplinary team (e.g., endocrinologists, neonatologists, urogynecologists, etc.). These conditions may lead to long-term reproductive, psychological, and sexual health consequences.

This chapter covers the relatively common congenital pelvic malformations that require vaginoplasty. The individual pathophysiology, clinical presentation, diagnosis, and management options, both conservative and surgical, will be presented. The common surgical techniques of (neo)vaginoplasty will be discussed.

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Author information

Authors and Affiliations

  1. Sexual Medicine and Genitourinary Reconstructive Surgery, McGill University Health Center, Montreal, QC, Canada

    Manuel Belmonte Chico Goerne

  2. McGill University, Montreal, QC, Canada

    David Bouhadana

  3. Department of Surgery and Pediatric surgery, McGill University Health Center and Montreal Children’s Hospital, Montreal, QC, Canada

    Mohamed El-Sherbiny

  4. Department of Surgery/Urology, McGill University Health Center and Lachine Hospital, Montreal, QC, Canada

    Mélanie Aubé-Peterkin

Authors
  1. Manuel Belmonte Chico Goerne
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  2. David Bouhadana
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  3. Mohamed El-Sherbiny
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  4. Mélanie Aubé-Peterkin
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Corresponding author

Correspondence to Mélanie Aubé-Peterkin .

Editor information

Editors and Affiliations

  1. University of Lisbon, Lisbon, Portugal

    Francisco E. Martins

  2. University of Oslo, Oslo, Norway

    Henriette Veiby Holm

  3. Memorial Sloan Kettering Cancer Center, New York, NY, USA

    Jaspreet S. Sandhu

  4. Eastern Virginia Medical School, Norfolk, VA, USA

    Kurt A McCammon

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Belmonte Chico Goerne, M., Bouhadana, D., El-Sherbiny, M., Aubé-Peterkin, M. (2023). (Neo) Vaginoplasty in Female Pelvic Congenital Anomalies. In: Martins, F.E., Holm, H.V., Sandhu, J.S., McCammon, K.A. (eds) Female Genitourinary and Pelvic Floor Reconstruction. Springer, Cham. https://doi.org/10.1007/978-3-031-19598-3_64

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  • DOI: https://doi.org/10.1007/978-3-031-19598-3_64

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