Abstract
Neurocutaneous melanosis (NCM) is a rare congenital non-inherited-embryonic neuroectodermal disease. Von Rokitansky is accredited in reporting the first description of the (NMS) in 1861. The hallmark of NCM is large bilateral hairy dark naevi with satellite naevi on the trunk and neck and benign or malignant melanocytic tumours in the letomininges of the central nervous system. The disorder is associated with a high mortality rate in early life. The diagnosis should be considered in neonates with large pigmented naevi and in those with more than three hairy dark naevi regardless of their sizes. This chapter describes the genetic, pathophysiology, clinical characteristics, and management options.
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Panteliadis, C.P. (2022). Neurocutaneous Melanosis. In: Panteliadis, C.P., Benjamin, R., Hagel, C. (eds) Neurocutaneous Disorders. Springer, Cham. https://doi.org/10.1007/978-3-030-87893-1_11
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