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Maladie de Rendu-Osler révélée par l’atteinte hépatique

Osler-Rendu-Weber disease: disease involving the liver

  • Cas Clinique / Case Report
  • Published:
Journal Africain d'Hépato-Gastroentérologie

Résumé

Nous rapportons l’observation d’un patient de 58 ans ayant une maladie de Rendu-Osler (MRO) avec atteinte hépatique asymptomatique révélée par une hépatosplénomégalie. Nous nous proposons de revoir les caractéristiques épidémiologiques, cliniques, diagnostiques, évolutives et thérapeutiques des malformations vasculaires hépatiques au cours de la MRO.

Abstract

We report the case of a 58-year-old patient with hepatic vascular malformations, revealing Osler-Rendu-Weber disease. We reviewed the main features of hepatic vascular malformations of Rendu-Osler disease, including epidemiology, diagnosis, outcome, and therapy.

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Authors and Affiliations

  1. Service de gastroentérologie et de médecine interne, hôpital militaire Moulay-Ismail, Meknès, Maroc

    T. Lamsiah, F. Z. El Hamdi, A. Zinebi, K. Moudden, M. Baaj & L. Hadri

  2. Service de radiologie, hôpital militaire Moulay-Ismail, Meknès, Maroc

    S. Belaabas & A. El Kharras

Authors
  1. T. Lamsiah
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  2. F. Z. El Hamdi
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  3. S. Belaabas
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  4. A. Zinebi
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  5. A. El Kharras
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  6. K. Moudden
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  7. M. Baaj
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  8. L. Hadri
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Correspondence to T. Lamsiah.

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Lamsiah, T., El Hamdi, F.Z., Belaabas, S. et al. Maladie de Rendu-Osler révélée par l’atteinte hépatique. J Afr Hepato Gastroenterol 10, 229–232 (2016). https://doi.org/10.1007/s12157-016-0684-2

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  • DOI: https://doi.org/10.1007/s12157-016-0684-2

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