Log in

When pulmonary arterial hypertension complicates connective tissue diseases: we still have not found what we are looking for

  • IM - COMMENTARY
  • Published:
Internal and Emergency Medicine Aims and scope Submit manuscript

This is a preview of subscription content, log in via an institution to check access.

Access this article

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Fig. 1

References

  1. Xanthouli P, Echampati I, Lorenz HM, Heussel CP, Benjamin N (2024) Respiratory involvement in connective tissue diseases. Eur J Intern Med 120:11–16. https://doi.org/10.1016/j.ejim.2023.09.016

    Article  PubMed  Google Scholar 

  2. Ghio S, D’Alto M, Badagliacca R, Vitulo P, Argiento P, Mulè M, Tuzzolino F, Scelsi L, Romeo E, Raineri C, Martino L, Tamburino C, Poscia R, Vizza CD (2017) Prognostic relevance of pulmonary arterial compliance after therapy initiation or escalation in patients with pulmonary arterial hypertension. Int J Cardiol 1(230):53–58. https://doi.org/10.1016/j.ijcard.2016.12.099

    Article  Google Scholar 

  3. D’Alto M, Badagliacca R, Lo Giudice F, Argiento P, Casu G, Corda M, Correale M, Ghio S, Greco A, Lattanzio M, Mercurio V, Paciocco G, Papa S, Prediletto R, Romeo E, Russo MG, Tayar A, Vitulo P, Vizza CD, Golino P, Naeije R (2020) Hemodynamics and risk assessment 2 years after the initiation of upfront ambrisentan-tadalafil in pulmonary arterial hypertension. J Heart Lung Transplant 39(12):1389–1397. https://doi.org/10.1016/j.healun.2020.08.016

    Article  PubMed  Google Scholar 

  4. Erdogan M, Esatoglu SN, KilickiranAvci B, Hatemi G (2024) Treatment of pulmonary arterial hypertension in patients with connective tissue diseases: a systematic review and meta-analysis. Intern Emerg Med. https://doi.org/10.1007/s11739-024-03539-1

    Article  PubMed  PubMed Central  Google Scholar 

  5. Rhee RL, Gabler NB, Sangani S, Praestgaard A, Merkel PA, Kawut SM (2015) Comparison of treatment response in idiopathic and connective tissue disease-associated pulmonary arterial hypertension. Am J Respir Crit Care Med 192(9):1111–1117. https://doi.org/10.1164/rccm.201507-1456OC

    Article  CAS  PubMed  PubMed Central  Google Scholar 

  6. Tedford RJ, Mudd JO, Girgis RE et al (2013) Right ventricular dysfunction in systemic sclerosis-associated pulmonary arterial hypertension. Circ Heart Fail 6(5):953–963. https://doi.org/10.1161/CIRCHEARTFAILURE.112.000008

    Article  CAS  PubMed  Google Scholar 

  7. Hoeper MM, Badesch DB, Ghofrani HA et al (2023) Phase 3 trial of sotatercept for treatment of pulmonary arterial hypertension. N Engl J Med 388(16):1478–1490. https://doi.org/10.1056/NEJMoa2213558

    Article  CAS  PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Corresponding author

Correspondence to Antonietta Gigante.

Ethics declarations

Conflict of interest

The authors declare that they have no conflict of interest.

Human and animal rights

This article does not contain any studies with human participants or animals performed by any of the authors.

Informed consent

For this type of study, formal consent is not required.

Additional information

Publisher's Note

Springer Nature remains neutral with regard to jurisdictional claims in published maps and institutional affiliations.

Rights and permissions

Reprints and permissions

About this article

Check for updates. Verify currency and authenticity via CrossMark

Cite this article

Gigante, A., Papa, S., Rosato, E. et al. When pulmonary arterial hypertension complicates connective tissue diseases: we still have not found what we are looking for. Intern Emerg Med 19, 883–884 (2024). https://doi.org/10.1007/s11739-024-03598-4

Download citation

  • Received:

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s11739-024-03598-4

Navigation