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References
Xanthouli P, Echampati I, Lorenz HM, Heussel CP, Benjamin N (2024) Respiratory involvement in connective tissue diseases. Eur J Intern Med 120:11–16. https://doi.org/10.1016/j.ejim.2023.09.016
Ghio S, D’Alto M, Badagliacca R, Vitulo P, Argiento P, Mulè M, Tuzzolino F, Scelsi L, Romeo E, Raineri C, Martino L, Tamburino C, Poscia R, Vizza CD (2017) Prognostic relevance of pulmonary arterial compliance after therapy initiation or escalation in patients with pulmonary arterial hypertension. Int J Cardiol 1(230):53–58. https://doi.org/10.1016/j.ijcard.2016.12.099
D’Alto M, Badagliacca R, Lo Giudice F, Argiento P, Casu G, Corda M, Correale M, Ghio S, Greco A, Lattanzio M, Mercurio V, Paciocco G, Papa S, Prediletto R, Romeo E, Russo MG, Tayar A, Vitulo P, Vizza CD, Golino P, Naeije R (2020) Hemodynamics and risk assessment 2 years after the initiation of upfront ambrisentan-tadalafil in pulmonary arterial hypertension. J Heart Lung Transplant 39(12):1389–1397. https://doi.org/10.1016/j.healun.2020.08.016
Erdogan M, Esatoglu SN, KilickiranAvci B, Hatemi G (2024) Treatment of pulmonary arterial hypertension in patients with connective tissue diseases: a systematic review and meta-analysis. Intern Emerg Med. https://doi.org/10.1007/s11739-024-03539-1
Rhee RL, Gabler NB, Sangani S, Praestgaard A, Merkel PA, Kawut SM (2015) Comparison of treatment response in idiopathic and connective tissue disease-associated pulmonary arterial hypertension. Am J Respir Crit Care Med 192(9):1111–1117. https://doi.org/10.1164/rccm.201507-1456OC
Tedford RJ, Mudd JO, Girgis RE et al (2013) Right ventricular dysfunction in systemic sclerosis-associated pulmonary arterial hypertension. Circ Heart Fail 6(5):953–963. https://doi.org/10.1161/CIRCHEARTFAILURE.112.000008
Hoeper MM, Badesch DB, Ghofrani HA et al (2023) Phase 3 trial of sotatercept for treatment of pulmonary arterial hypertension. N Engl J Med 388(16):1478–1490. https://doi.org/10.1056/NEJMoa2213558
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Gigante, A., Papa, S., Rosato, E. et al. When pulmonary arterial hypertension complicates connective tissue diseases: we still have not found what we are looking for. Intern Emerg Med 19, 883–884 (2024). https://doi.org/10.1007/s11739-024-03598-4
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DOI: https://doi.org/10.1007/s11739-024-03598-4