Abstract
Primary papillary epithelial tumor of the sella (PPETS) is a newly described tumor entity with prototypical location in the sella. Only two case series with ten cases have been described so far. These tumours have a typical papillary architecture with bland nuclear features, TTF-1 immunopositivity and low MIB-1-labelling index. Many of these tumours were previously assigned under the category of ‘ectopic choroid plexus papilloma’. PPETS expands the group of TTF-1 positive tumours of the central nervous system. Histomorphology plays an essential role in making this diagnosis. We report a case of 44-year-old female with a sellar mass lesion, who presented with progressive loss of vision and diagnosed as primary papillary epithelial tumor.
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Rima, S., Rao, S., Nigam, P. et al. Primary papillary epithelial tumor of the sella: a case report of an emerging tumor type. Brain Tumor Pathol 41, 30–34 (2024). https://doi.org/10.1007/s10014-023-00472-7
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DOI: https://doi.org/10.1007/s10014-023-00472-7