Abstract
Most cases of craniosynostosis are diagnosed during early infancy, but occasionally craniosynostosis evolves with minimal cranial involvement and goes unnoticed until late childhood. Seemingly these mild forms of craniosynostosis cause few, if any, symptoms of neurological involvement. We describe the cases of a 9-year-old girl and a 6-year-old boy who presented with evident signs of raised intracranial pressure (ICP), together with a negligible skull deformity. We have termed these cases as occult craniosynostosis. Differential diagnosis in our patients was established against known causes of benign intracranial hypertension. Bilateral expanding craniotomies afforded total relief from the symptoms and signs of raised ICP. Neurosurgeons treating children with symptoms and signs of benign intracranial hypertension should be aware of the possibility of minimal forms of craniosynostosis evolving with marked manifestations of raised ICP.
Similar content being viewed by others
Author information
Authors and Affiliations
Additional information
Received: 18 May 1998
Rights and permissions
About this article
Cite this article
Martínez-Lage, J., Alamo, L. & Poza, M. Raised intracranial pressure in minimal forms of craniosynostosis. Child's Nerv Syst 15, 11–15 (1999). https://doi.org/10.1007/s003810050319
Issue Date:
DOI: https://doi.org/10.1007/s003810050319