Zusammenfassung
Das seltene Krankheitsbild des systemischen Kapillarlecksyndroms verursacht Phasen des hypovolämischen Schocks aufgrund einer stark erhöhten Flüssigkeitsverschiebung in das Interstitium. Wegweisende Laborparameter sind Hämokonzentration, Hypoalbuminämie und eine monoklonale Gammopathie. Eine seltene Manifestation dieses Krankheitsbildes ist das Kompartmentsyndrom mit Rhabdomyolyse und akutem Nierenversagen. Wir beschreiben den Fall eines Patienten, der auf dem Boden eines systemischen Kapillarlecksyndroms ein Kompartmentsyndrom beider Unterschenkel und des linken Unterarms erlitt und diskutieren den pathophysiologischen Hintergrund.
Abstract
Systemic capillary leak syndrome is a rare disorder which causes recurrent episodes of hypovolemic shock due to a markedly increased plasma shift into the interstitium. Hemoconcentration, hypoalbumimenia and a monoclonal gammopathy are characteristic laboratory findings. A rare manifestation of this disease is a compartment syndrome with rhabdomyolysis and acute renal failure. We describe a patient who suffers from a compartment syndrome of both lower legs and the left forearm secondary to systemic capillary leak syndrome, and discuss the pathophysiological background.
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Balcarek, P., Frosch, KH., Quintel, M. et al. Systemisches Kapillarlecksyndrom als Ursache eines Kompartmentsyndroms beider Unterschenkel und eines Unterarms. Unfallchirurg 108, 770–776 (2005). https://doi.org/10.1007/s00113-005-0918-z
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DOI: https://doi.org/10.1007/s00113-005-0918-z