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Duplication Anomalies of the Kidney and Ureters

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Congenital Anomalies of the Kidney and Urinary Tract

Abstract

Duplicated kidney and ureters can be one of the more controversial urological anomalies. They can range from interesting radiological findings to clinical issues such as ectopia, obstructive ureteroceles, and vesicoureteral reflux. This chapter focuses on the embryological origins of these anomalies and their common presentations. A comprehensive review of proper diagnostic evaluation ensues. Although management algorithms are presented, one must keep in mind that the best management for every child is one that is tailored to his or her specific anatomy. Nevertheless, general treatment guidelines consist of preventing morbidity from urinary tract infections, preserving adequate renal function and urinary continence, and eliminating complications associated with obstruction or vesicoureteral reflux.

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Abbreviations

IVP:

Intravenous pyelogram

UP:

Ureteropyelostomy

UTI:

Urinary tract infection

UU:

Ureteroureterostomy

VCUG:

Voiding cystourethrogram

VUR:

Vesicoureteral reflux

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Acknowledgements

We would like to acknowledge Nikta Khajeh, a UCI undergraduate student completing a urology clinical research internship, who has skillfully hand-drawn all the drawings included in this chapter. We are thankful for her contribution.

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Authors and Affiliations

  1. Department of Urology, University of California, Irvine, CA, USA

    Orchid Djahangirian M.D. & Antoine Khoury M.D., F.R.C.S.C., F.A.A.P.

  2. Department of Urology, Children’s Hospital of Orange County, 505 S Main St #100, Orange, CA, 92868, USA

    Orchid Djahangirian M.D.

  3. Children’s Hospital of Orange County, Orange, CA, USA

    Antoine Khoury M.D., F.R.C.S.C., F.A.A.P.

Authors
  1. Orchid Djahangirian M.D.
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  2. Antoine Khoury M.D., F.R.C.S.C., F.A.A.P.
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Correspondence to Antoine Khoury M.D., F.R.C.S.C., F.A.A.P. .

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Editors and Affiliations

  1. Department of Pediatrics, Georgetown University Medical Center, Washington, District of Columbia, USA

    Amin J. Barakat

  2. Division of Pediatric Urology, Children’, George Washington University School of M, Washington, District of Columbia, USA

    H. Gil Rushton

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Djahangirian, O., Khoury, A. (2016). Duplication Anomalies of the Kidney and Ureters. In: Barakat, A., Rushton, H. (eds) Congenital Anomalies of the Kidney and Urinary Tract. Springer, Cham. https://doi.org/10.1007/978-3-319-29219-9_8

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  • DOI: https://doi.org/10.1007/978-3-319-29219-9_8

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