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Clinical and Surgical Management of Pediatric Fibroinflammatory Diseases and Tumors of the Head and Neck

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Pediatric Head and Neck Textbook

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Abstract

Fibroinflammatory tumors are rare head and neck tumor in children. They are classified by the WHO as intermediate tumors meaning that although they are benign and do not metastasize, they are very locally aggressive. This interesting group of tumors mimics malignant disease such as sarcomas, but is often managed differently from malignant tumors of the head and neck. Fibroinflammatory tumors include aggressive fibromatosis, infantile fibrosarcoma, and inflammatory myofibroblastic tumors. The classification, clinical presentation, radiological features, and approach to surgical and adjuvant management will be described in this chapter.

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Authors and Affiliations

  1. Department of Paediatric ENT, Royal Hospital for Sick Children, Edinburgh, UK

    Alok Sharma

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  1. Alok Sharma
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Editors and Affiliations

  1. Department of Otolaryngology – Head & Neck Surgery, University of Toronto, Toronto, ON, Canada

    Paolo Campisi

  2. Department of Otolaryngology – Head & Neck Surgery, University of Toronto, Toronto, ON, Canada

    Vito Forte

  3. Division of Pathology, Paediatric Laboratory, Hospital for Sick Children Division of Pathology, Toronto, ON, Canada

    Bo-Yee Ngan

  4. Division of Pathology, Department of Laboratory Medicine (retired), Hospital for Sick Children, Toronto, ON, Canada

    Glenn Taylor

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Sharma, A. (2021). Clinical and Surgical Management of Pediatric Fibroinflammatory Diseases and Tumors of the Head and Neck. In: Campisi, P., Forte, V., Ngan, BY., Taylor, G. (eds) Pediatric Head and Neck Textbook. Springer, Cham. https://doi.org/10.1007/978-3-030-59265-3_26

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