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Venous Malformations and Associated Syndromes: Diagnosis and Management

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Vascular Anomalies

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Abstract

Venous malformations are congenital low-flow vascular malformations. Venous malformations commonly present in the skin and superficial soft tissues; they can involve deeper structures. Venous malformations are associated with other vascular anomaly syndromes as well. Common presenting symptoms include swelling, pain, mass effect, and psychosocial stressors. Coagulopathy is observed with diffuse and multifocal lesions. Ultrasonography and magnetic resonance imaging are useful adjuncts for diagnosis and understanding extent and relationship to adjacent structures. Mainstays of therapy include expectant management, compression, pain control, sclerotherapy, and surgical resection. Multimodal and interdisciplinary care is crucial to provide comprehensive care to patients with venous malformations.

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Author information

Authors and Affiliations

  1. Division of Pediatric Surgery, Vascular Anomalies Center, University of Colorado School of Medicine, Children’s Hospital Colorado, Aurora, CO, USA

    Ann M. Kulungowski

  2. Department of Radiology and Medical Imaging, Hemangioma and Vascular Malformation Center, University of Cincinnati School of Medicine, Cincinnati Children’s Hospital Medical Center, Cincinnati, OH, USA

    Manish N. Patel

  3. Department of Surgery, Vascular Anomalies Center, Harvard Medical School, Children’s Hospital Boston, Boston, MA, USA

    Steven J. Fishman

Authors
  1. Ann M. Kulungowski
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  2. Manish N. Patel
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  3. Steven J. Fishman
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Corresponding author

Correspondence to Ann M. Kulungowski .

Editor information

Editors and Affiliations

  1. Dana-Farber Cancer Institute, Boston Children’s Hospital, Boston, MA, USA

    Cameron C. Trenor III

  2. Dana-Farber Cancer Institute, Boston Children’s Hospital, Boston, MA, USA

    Denise M. Adams

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Kulungowski, A.M., Patel, M.N., Fishman, S.J. (2020). Venous Malformations and Associated Syndromes: Diagnosis and Management. In: Trenor III, C., Adams, D. (eds) Vascular Anomalies. Springer, Cham. https://doi.org/10.1007/978-3-030-25624-1_9

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  • DOI: https://doi.org/10.1007/978-3-030-25624-1_9

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