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Hirschsprung’s Disease and Anorectal Manometry

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Hirschsprung's Disease and Allied Disorders

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Abstract

‘A properly functioning rectum is an unappreciated gift of the greatest price’(Potts, The surgeon and the child. WB Saunders Company, Philadelphia, 1959). Anorectal physiology (ARP) has been around for almost 140 years and has been greatly utilised in patients with Hirschsprung’s disease (HSCR) for the purposes of diagnosis and post-operative bowel function assessment and to enhance the understanding of disease-specific conditions (such as HSCR, anorectal malformation and idiopathic constipation).

This chapter will review the use of ARP in patients with HSCR. It has been a lengthy journey from Gower’s first descriptions of the anorectum to today’s high-resolution ARP. New methods for visualising the anorectum has revolutionised our understanding of its pathophysiology.

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  1. Department of Paediatric Surgery, The Royal London Hospital, Barts Health, Whitechapel, London, UK

    Eleni Athanasakos & Stewart Cleeve

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  1. Eleni Athanasakos
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    Prem Puri

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Athanasakos, E., Cleeve, S. (2019). Hirschsprung’s Disease and Anorectal Manometry. In: Puri, P. (eds) Hirschsprung's Disease and Allied Disorders. Springer, Cham. https://doi.org/10.1007/978-3-030-15647-3_15

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