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How I Manage Sickle Cell Retinopathy
Purpose of ReviewWe describe our current approach to sickle cell retinopathy screening, evaluation, treatment, and surgical intervention.
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Risk factors associated with sickle cell retinopathy: findings from the Cooperative Study of Sickle Cell Disease
BackgroundSickle cell retinopathy (SCR) is one of the most important ocular manifestations of sickle cell disease (SCD). This study aims to assess...
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Paediatric sickle cell disease presenting with hepatobiliary symptoms—a case presentation and brief literature review
BackgroundSickle hepatopathy is the hepatobiliary dysfunction associated with sickle cell disease. It has a varied spectrum ranging from asymptomatic...
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Aerobic physical capacity and health-related quality of life in children with sickle cell disease
BackgroundAerobic fitness is a predictor of cardiovascular health which correlates with health-related quality of life in the general population. The...
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Bone Turnover Markers Levels in a Cohort of Egyptian Children with Sickle Cell Disease
Bony complications are variable and common in sickle cell disease. Bone turnover markers are a reflection of bone new bone formation or degradation....
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The nephropathy of sickle cell trait and sickle cell disease
Sickle cell syndromes, including sickle cell disease (SCD) and sickle cell trait, are associated with multiple kidney abnormalities. Young patients...
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Prevalence and factors associated with hypothyroidism in children with sickle cell anemia aged 6 months − 17 years attending the Sickle Cell Clinic, Mulago Hospital, Uganda; a cross-sectional study
PurposeHypothyroidism has been reported at a prevalence of 6% in children and adolescents with Sickle cell anemia. In this study, we determined the...
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Survival of total hip arthroplasty (THA) in sickle cell disease
BackgroundThe objective of this study was to evaluate the outcome of THA done in patients with sickle cell disease at a single center, and compare...
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Evaluation of peripheral blood inflammatory biomarkers in sickle cell disease with and without retinopathy
BackgroundThe aim of this study was to evaluate the clinical significance of blood-cell associated inflammation markers in patients with sickle cell...
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Transforming growth factor-β1: relation between its single-nucleotide genetic variants and sickle cell nephropathy
BackgroundSickle cell nephropathy is a complication of sickle cell disease characterized by functional abnormalities of the kidney and glomeruli. Our...
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Jaundice in a Child with Sickle Cell Anemia: A Case Based Approach
Sickle cell anemia (SCA) is an autosomal recessive disorder caused by a mutation in beta globin gene. Hepatobiliary system is affected in 10-40% of...
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Evaluation of knowledge of priapism in sickle cell patients in Senegal
PurposeErectile dysfunction is a dreadful complication of priapism especially with delay in diagnosis and management. The lack of awareness of...
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Update on the practice of premarital screening for sickle cell traits in Africa: a systematic review and meta-analysis
BackgroundScreening for sickle cell traits before marriage or producing children is one of the outstanding preventive measures for sickle cell...
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Cutaneous manifestations of sickle cell disease: an updated review
Sickle cell disease is a common and highly morbid genetic condition that is characterized by multi-system involvement, including numerous cutaneous...
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Utility of Low-cost Paper Based Haemoglobin Solubility Test for the Rapid Diagnosis of Sickle Cell Disease
In this study, we describe and compare a simple, rapid, low cost, point-of-care diagnostic paper-based test for screening of sickle cell disease,...
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Sickle cell trait in São Tomé e Príncipe: a population-based prevalence study in women of reproductive age
BackgroundSickle Cell Disorder is Africa’s most prevalent genetic disease. Yet, it remains a neglected condition, with high mortality under-five, and...
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Proliferative Sickle Cell Retinopathy: A Patient and a Physician’s Perspective on Quality of Life and Quality of Eye Care
The impact of visual impairment in the context of sickle cell disease is poorly understood. Despite the significant advancements over the past...
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Death due to sickle cell crisis: a case report
Sickle cell disease (SCD) is the most common hereditary hemoglobinopathy worldwide. It results in characteristic acute and chronic findings on...
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Evaluation of pulmonary function in Egyptian children with sickle cell disease: a single center study
BackgroundAmong inherited blood diseases, sickle cell disease (SCD) is the most common, and its prevalence is rising worldwide. People with SCD often...
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Enuresis and overactive bladder in sickle cell patients: a narrative review of the literature
ObjectiveThe aim of this review is to clarify the prevalence, pathophysiology and clinical presentation of enuresis and overactive bladder in sickle...
