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Pathogenesis and treatment of a giant occipital bone defect with meningoencephalocele in an NF1 child: case report and review of the literature
Autosomal dominantly inherited neurofibromatosis type I (NF1) is a systemic disorder caused by a mutation of a gene on chromosome 17q11.2 and...
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Anterior mediastinal neurofibrosarcoma—a rare manifestation of neurofibromatosis type-1
Anterior mediastinal neurofibroma and neurofibrosarcoma form a rare class of tumors seen in patients of neurofibromatosis. We describe a case of...
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NTRK-rearranged spindle cell sarcoma of the uterine cervix with a novel NUMA1::NTRK1 fusion
NTRK -rearranged uterine sarcoma is a recently described entity that represents a subset of uterine sarcomas with distinct clinicopathological...
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Pterygopalatine-Infratemporal Fossa Hydatid Cyst Resembling Cystic Tumor
Hydatid cyst is an endemic disease in Mediterranean and Middle Eastern countries, Eastern European countries, East Africa, China, New Zealand,...
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A Rare Presentation of Recurrent Malignant Peripheral Nerve Sheath Tumor with Glandular Differentiation—A Case Report
Malignant peripheral nerve sheath tumors (MPNST) are rare heterogeneous group of soft tissue neoplasms. In most cases, they originate within the...
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Cardiac synovial sarcoma masquerading as effusive constrictive pericarditis
Primary cardiac synovial sarcoma is a rare entity, arising from the pericardium or the chambers of the heart. It presents in the 4 th decade of life...
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Malignant Chest Wall Tumors: Complex Defects and Their Management—A Review of 181 Cases
BackgroundChest wall tumors are a heterogeneous group of tumors that are managed by surgeons from diverse specialties. Due to their rarity, there is...
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Impact of neurofibromatosis type 1 on quality of life using the Skindex-29 questionnaire quality of life in NF1
BackgroundNeurofibromatosis type 1 (NF1) is one of the most common RASopathies predisposing affected patients to melanic lesions and benign tumors....
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Surgical management of craniospinal axis malignant peripheral nerve sheath tumors: a single-institution experience and literature review
BackgroundMalignant peripheral nerve sheath tumor (MPNST) is an exceedingly rare and aggressive tumor, with limited literature on its management....
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Transanal endoscopic microsurgery technique: an acceptable approach for retrorectal tumors
IntroductionRetrorectal lesions (RRLs) are rare lesions that originate from the tissue present in the retrorectal space. The gold standard of care is...
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Survival outcomes of malignant peripheral nerve sheath tumors (MPNSTs) with and without neurofibromatosis type I (NF1): a meta-analysis
IntroductionMalignant peripheral nerve sheath tumors (MPNSTs) are malignancies that demonstrate nerve sheath differentiation in the peripheral...
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Surgery for primary malignant tumors of the abdominal wall: experiences of three African surgical oncology units and review of the literature
Background and objectivesTumors of the abdominal wall are uncommon but diverse. The surgical challenge is double. The tumor must be completely...
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Predictors of postoperative performance status after surgical management of infratemporal fossa malignancies
Infratemporal fossa (ITF) tumors are difficult to access surgically due to anatomical constraints. Moreover, aggressive ITF carcinomas and sarcomas...
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Extremity high-grade sarcomas in elderly patients, are they candidates for surgery? Experience in a sarcoma referral center
The number of elderly patients diagnosed with cancer is increasing. However, knowledge regarding cancer in elderly patients is very scarce. The aim...
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Brain metastases of sarcoma: a rare phenomenon in rare tumours
The usual site for distant metastases of sarcoma is lungs, while brain metastasis (BM) occurs much less frequently and usually late in the disease...
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Malignant peripheral nerve sheath tumour in an unusual location of the urinary bladder: case report and review of literature
BackgroundMalignant peripheral nerve sheath tumour (MPNST) is a rare malignant soft tissue neoplasm of ectomesenchymal origin. They usually arise...
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Traveling to Receive Treatment for Extremity Soft Tissue Sarcomas: Is it worth the drive?
BackgroundRegionalization of sarcoma care may improve outcomes. Concerns exist regarding the burdens of travel and its effects on care. We evaluate...
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The impact of expanded endoscopic approaches on oncologic and functional outcomes for clival malignancies:a case series
IntroductionClival malignancies pose particular surgical challenges due to complex skull base anatomy and the involvement of vital neurovascular...