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Lung adenocarcinoma discovered during the follow-up of lung-dominant connective tissue disease: a case report and literature review
Interstitial lung disease (ILD) can lead to lung cancer, which brings great challenges to differential diagnosis and comprehensive treatment....
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Real world experience with nintedanib in connective tissue disease-related interstitial lung disease: a retrospective cohort study
Various connective tissue diseases tend to affect specific organs, lungs being the organ with the most serious repercussions and consequences. The...
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Can transbronchial lung cryobiopsy benefit adaptive treatment strategies in connective tissue disease-associated interstitial lung disease?
BackgroundSome patients with connective tissue disease (CTD)-associated interstitial lung disease (ILD) progress to pulmonary fibrosis over their...
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Management of Connective Tissue Disease–related Interstitial Lung Disease
Purpose of ReviewThis review aims to collate current evidence on the screening, diagnosis, and treatment of various connective tissue disease...
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Diagnosis and treatment of cardiovascular disease in patients with heritable connective tissue disorders or heritable thoracic aortic diseases
Patients with heritable connective tissue disorders (HCTDs), represented by Marfan syndrome, can develop fatal aortic and/or arterial complications...
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Cardiac dysfunction in mixed connective tissue disease: a nationwide observational study
We aimed to identify cardiac function in patients with established mixed connective tissue disease (MCTD). This was a cross-sectional case–control...
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The enigma of mixed connective tissue disease—challenges in routine care
ObjectivesAs a rare and heterogeneous disease, mixed connective tissue disease (MCTD) represents a challenge. Herein, we aimed to unravel potential...
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Pediatric mixed connective tissue disease versus other overlap syndromes: a retrospective multicenter cohort study
Pediatric mixed connective tissue disease (MCTD) is a subgroup of overlap syndromes. We aimed to compare the characteristics and outcomes in children...
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Pulmonary hypertension in connective tissue diseases: epidemiology, pathogenesis, and treatment
AbstractPulmonary hypertension (PH) is a clinical condition characterized by increased pulmonary arterial pressure arising from a heterogeneous range...
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Relationship between type of skin lesions and nailfold capillaroscopy pattern in mixed connective tissue disease
IntroductionMixed connective tissue disease (MCTD) is a rare disease with clinical picture consisted of multiple organ manifestations, including skin...
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Fibrosing Interstitial Lung Disease in Children: An HRCT-Based Analysis
ObjectiveTo determine high resolution CT (HRCT) patterns of pulmonary fibrosis (PF) in children; and their etiological correlates.
Methods ...
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Emerging Treatments for Childhood Interstitial Lung Disease
Childhood interstitial lung disease (chILD) is a large and heterogeneous group of disorders characterized by diffuse lung parenchymal markings on...
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Thoracoabdominal aortic aneurysm in connective tissue disorder patients
Connective tissue disorders (CTDs) are a group of genetically triggered diseases in which the primary defect involves collagen and elastin protein...
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Interstitial lung disease in the newborn
Although relatively rare, interstitial lung diseases may present with respiratory distress in the newborn period. Most commonly these include...
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Real-World Treatment Patterns Among Patients with Connective Tissue Disorder-Related Pulmonary Arterial Hypertension in the United States: A Retrospective Claims-Based Analysis
IntroductionConnective tissue disorders (CTDs) are the most frequent diseases associated with pulmonary arterial hypertension (PAH). Despite advances...
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Capillaroscopy as a diagnostic tool in the diagnosis of mixed connective tissue disease (MCTD): a case report
BackgroundThe concept of mixed connective tissue disease (MCTD) as a unique connective tissue disease has endured for half a century. Disease onset...
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Single nucleotide variants around the connective tissue growth factor (CTGF/CCN2) gene and their association with multiple sclerosis risk, disability scores, and rate of disease progression
BackgroundThis study aimed to explore the possible association of single nucleotide polymorphisms (SNPs) in the upstream (rs9402373) and downstream...
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Acute exacerbation of interstitial lung disease associated with rheumatic disease
Interstitial lung disease (ILD) is a cause of morbidity and mortality in patients with rheumatic diseases, such as connective-tissue diseases,...
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Interstitial lung disease is a dominant feature in patients with circulating myositis-specific antibodies
BackgroundMany patients with polymyositis (PM) or dermatomyositis (DM) have circulating myositis-specific antibodies (MSAs). Interstitial lung...
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Effects of tissue degradation by collagenase and elastase on the biaxial mechanics of porcine airways
BackgroundCommon respiratory illnesses, such as emphysema and chronic obstructive pulmonary disease, are characterized by connective tissue damage...
