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The effect of respiratory muscle training on children and adolescents with cystic fibrosis: a systematic review and meta-analysis
BackgroundCystic fibrosis is a chronic genetic disease that can affect the function of the respiratory system. Previous reviews of the effects of...
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Vitamin D deficiency in patients with cystic fibrosis: a systematic review and meta-analysis
AimVitamin D is a prominent modulator of immunity and respiratory function. It plays a vital role in respiratory diseases such as cystic fibrosis...
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Increasing incidence rate of breast cancer in cystic fibrosis - relationship between pathogenesis, oncogenesis and prediction of the treatment effect in the context of worse clinical outcome and prognosis of cystic fibrosis due to estrogens
Cystic fibrosis (CF) is the most common genetic disease in the Caucasion population. Thanks to the CFTR modulators therapy, life expectancy will...
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The efficacy of azithromycin to prevent exacerbation of non-cystic fibrosis bronchiectasis: a meta-analysis of randomized controlled studies
IntroductionThe efficacy of azithromycin to prevent exacerbation for non-cystic fibrosis bronchiectasis remains controversial. We conduct this...
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Fractional Exhalation Nitric Oxide (FeNO) changes in cystic fibrosis patients induced by compound honey syrup: a pretest–posttest clinical trial
ObjectiveTo evaluate the effect of Persian medicine Syrup ‘compound honey syrup (CHS)’ on fractional exhalation nitric oxide (FENO) changes in...
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Cystic Fibrosis and Sleep Circadian Rhythms
Cystic fibrosis (CF) is due to a mutation in the cystic fibrosis transmembrane conductance regulator gene (CFTR), which leads to unusual water and...
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A systematic review of the clinical impact of small colony variants in patients with cystic fibrosis
BackgroundCystic fibrosis (CF) is a life-limiting disorder that is characterised by respiratory tract inflammation that is mediated by a range of...
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Depression and anxiety prevalence in people with cystic fibrosis and their caregivers: a systematic review and meta-analysis
BackgroundPrevalence of depression and anxiety in people with cystic fibrosis (PwCF) and their caregivers is high, however, results have been...
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Comparison of respiratory pathogen colonization and antimicrobial susceptibility in people with cystic fibrosis bronchiectasis versus non-cystic fibrosis bronchiectasis: a protocol for a systematic review
BackgroundBoth cystic fibrosis (CF) and non-cystic fibrosis bronchiectasis are characterized by permanent bronchial dilation, impaired mucociliary...
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High Hydrostatic Pressure Exacerbates Bladder Fibrosis through Activating Piezo1
ObjectiveBladder outlet obstruction (BOO) results in significant fibrosis in the chronic stage and elevated bladder pressure. Piezo1 is a type of...
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Novel mutation c.1210-3C > G in cis with a poly-T tract of 5T affects CFTR mRNA splicing in a Chinese patient with cystic fibrosis
Cystic fibrosis (CF) is a rare autosomal recessive disease with only one pathogenic gene cystic fibrosis transmembrane conductance regulator ( CFTR )....
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A systematic review of the research progress of traditional Chinese medicine against pulmonary fibrosis: from a pharmacological perspective
Pulmonary fibrosis is a chronic progressive interstitial lung disease caused by a variety of etiologies. The disease can eventually lead to...
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The impact of physical activity and exercise interventions for physical health in people with cystic fibrosis: protocol for a systematic review
BackgroundCystic fibrosis (CF) is a genetically inherited, life-limiting condition, affecting ~90,000 people globally. Physical activity (PA) and...
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What Do We Need to Know About Rising Rates of Idiopathic Pulmonary Fibrosis? A Narrative Review and Update
The most common type of idiopathic interstitial pneumonia is idiopathic pulmonary fibrosis (IPF), an irreversible, progressive disorder that has...
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Predictors of Malnutrition in Children with Cystic Fibrosis
ObjectiveTo determine occurrence of malnutrition in children with cystic fibrosis and identify predictors of malnutrition at time of enrolment and...
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The Therapeutic Effect of Bleomycin Sclerotherapy in Vascular Malformations
Sclerotherapy is a frequently employed technique for treating vascular malformations. Bleomycin is a sclerosant that has demonstrated efficacy and...
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Approaching two decades of cystic fibrosis research in Qatar: a historical perspective and future directions
Cystic fibrosis (CF) is a genetic disease caused by a defect of CF transmembrane conductance regulator (CFTR) gene. CF affects multiple systems,...
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H. sinensis mycelium inhibits epithelial-mesenchymal transition by inactivating the midkine pathway in pulmonary fibrosis
The medical fungus Hirsutella sinensis has been used as a Chinese folk health supplement because of its immunomodulatory properties. Our previous...
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Mutational Spectrum of the CFTR Gene in the Kazakhstan Population
ObjectiveTo study the frequency and spectrum of CFTR gene variants in different ethnic groups of Kazakhstan.
MethodsWe reviewed the records of 58...
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Aquagenic Wrinkling of Skin: A Screening Test for Cystic Fibrosis
ObjectiveTo study the utility of aquagenic wrinkling as screening test for children with cystic fibrosis.
DesignEvaluation of diagnostic test.
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