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Chapter and Conference Paper
Fatty Acid Metabolism in Cultured Skin Fibroblasts from Patients with Peroxisomal Disorders: Lignoceroyl-CoA Ligase Deficiency in Childhood Adrenoleukodystrophy
We have previously reported that the peroxisomal B-oxidation system for very long chain (>C22) fatty acids is defective in the peroxisomal disorders, adrenoleukodystrophy (ALD) and Zellweger’s cerebro-hepato-rena...