Synonyms
Diffuse interstitial lung disease from unknown causes; Diffuse parenchymal lung disease from unknown causes; Idiopathic interstitial lung diseases
Definition
The term “idiopathic interstitial lung diseases” is applied to a group of disorders with distinct histological and radiological appearances and without a known cause. These disorders essentially include sarcoidosis, lymphangioleiomyomatosis, pulmonary alveolar proteinosis, eosinophilic pneumonia, and idiopathic interstitial pneumonias (IIPs).
Idiopathic Interstitial Pneumonias
Pathology/Histopathology
The evolution of the classification of the IIPs over time has culminated in seven entities: idiopathic pulmonary fibrosis (IPF), corresponding to the pathology of usual interstitial pneumonia (UIP); nonspecific interstitial pneumonia (NSIP); desquamative interstitial pneumonia (DIP); respiratory bronchiolitis‐associated interstitial lung disease (RBILD); cryptogenic organizing pneumonia (COP), formerly known as...
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Bibliography
American Thoracic Society/European Respiratory Society (2002) International multidisciplinary consensus classification of the idiopathic interstitial pneumonias. Am J Respir Crit Care Med 165:277–304
Screaton NJ, Hiorns MP, Lee KS et al (2005) Serial high resolution CT in non‐specific interstitial pneumonia: prognostic value of the initial pattern. Clin Radiol 60:96–104
Lynch DA, Travis WD, Muller NL et al (2005) Idiopathic interstitial pneumonias: CT features. Radiology 236:10–21
Koyama T, Ueda H, Togashi K et al (2004) Radiologic manifestations of sarcoidosis in various organs. Radiographics 24:87–104
Nishimura K, Itoh H, Kitaichi M et al (1993) Pulmonary sarcoidosis: correlation of CT and histopathologic findings. Radiology 189:105–109
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© 2008 Springer-Verlag Berlin Heidelberg New York
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Sverzellati, N., Hansell, D.M. (2008). Interstitial Lung Diseases, Unknown Etiology. In: Baert, A.L. (eds) Encyclopedia of Diagnostic Imaging. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-35280-8_1288
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DOI: https://doi.org/10.1007/978-3-540-35280-8_1288
Publisher Name: Springer, Berlin, Heidelberg
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