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New Therapies

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Dermatology in Five Continents

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Abstract

We have recently identified and treated three patients with severe α-1-antitrypsin deficiency who developed progressive, destructive panniculitis. In addition, 3 patients with heterozygous, α-1-antitrypsin deficiency and panniculitis have been evaluated and followed after treatment was instituted. Therapeutic options for homozygous and heterozygous α-1-antitrypsin deficiency patients who develop panniculitis of varying severity will be presented.

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Author information

Authors and Affiliations

  1. Clinic for Dermatology and Venerology, University Hospital, Innsbruck, Austria

    P. Fritsch (Chairman)

  2. Department of Dermatology, Mayo Clinic, Rochester, Minnesota, USA

    S. Muller (Co-Chairman), M. R. Pittelkow, W. P. D. Su, K. C. Smith & R. K. Winkelmann

  3. Department of Dermatology, University of Gothenburg, Gothenburg, Sweden

    G. Swanbeck (Co-Chairman)

  4. Department of Dermatology, University Hospital Utrecht, Utrecht, The Netherlands

    H. Baart de la Faille & H. van Weelden

  5. Department of Gastroenterology, University Hospital Utrecht, Utrecht, The Netherlands

    J. van Hattum

  6. Institute of Pathology, Division of Electron Microscopy, University Hospital Utrecht, Utrecht, The Netherlands

    L. H. P. M. Rademakers

  7. Department of International Medicine II, University Hospital Rotterdam, Rotterdam, The Netherlands

    J. W. O. van den Berg

  8. Department of Dermatology, University of Gothenburg, Sahlgren’s Hospital, Gothenburg, Sweden

    J. Faergemann

  9. Department of Dermatology, University of Düsseldorf, Düsseldorf, FR Germany

    E. Hölzle

  10. Department of Dermatology, University of Innsbruck, Innsbruck, Austria

    J. Auböck

Authors
  1. P. Fritsch
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  2. S. Muller
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  3. G. Swanbeck
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  4. M. R. Pittelkow
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  5. W. P. D. Su
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  6. K. C. Smith
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  7. R. K. Winkelmann
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  8. H. Baart de la Faille
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  9. J. van Hattum
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  10. L. H. P. M. Rademakers
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  11. H. van Weelden
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  12. J. W. O. van den Berg
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  13. J. Faergemann
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  14. E. Hölzle
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  15. J. Auböck
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Editor information

Editors and Affiliations

  1. Universitäts-Hautklinik und Poliklinik, Klinikum Steglitz der Freien Universität, Hindenburgdamm 30, D-1000, Berlin 45, Federal Republic of Germany

    Constantin E. Orfanos (CMD — Scientific Secretariat), Rudolf Stadler (CMD — Scientific Secretariat) & Harald Gollnick (CMD — Scientific Secretariat) (CMD — Scientific Secretariat),  (CMD — Scientific Secretariat) &  (CMD — Scientific Secretariat)

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© 1988 Springer-Verlag Berlin Heidelberg

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Fritsch, P. et al. (1988). New Therapies. In: Orfanos, C.E., Stadler, R., Gollnick, H. (eds) Dermatology in Five Continents. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-83360-1_55

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  • DOI: https://doi.org/10.1007/978-3-642-83360-1_55

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-83362-5

  • Online ISBN: 978-3-642-83360-1

  • eBook Packages: Springer Book Archive

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