Abstract
This chapter provides a detailed exploration of embryonal tumors. It covers a range of tumor types, including medulloblastomas, embryonal tumors with multilayered rosettes (ETMR), and atypical teratoid/rhabdoid tumors (AT/RTs). It offers insights into their definition, epidemiology, pathology, molecular genetics, etiology, and clinical presentation. It further addresses staging and classification, diagnostic procedures, and various treatment options and considerations. The critical aspects of recurrence, follow-up, and prognosis are also discussed. This chapter serves to facilitate a well-structured approach to understanding and managing these tumors in the field of surgical neuro-oncology.
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Notes
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Near total resection: <1.5 cm2 on axial-plane early postop MRI. This criterion is controversial as much of the data is from the CT era.
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ElGhamry, A.M.N., Al-Khazaali, Y.M., Alaraji, Z.A., Hoz, S.S. (2024). Embryonal Tumors. In: Hoz, S.S., et al. Surgical Neuro-Oncology. Springer, Cham. https://doi.org/10.1007/978-3-031-53642-7_10
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