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Giant Stomach Secondary to Juvenile Polyposis Syndrome

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Journal of Gastrointestinal Surgery

Abstract

Introduction

Juvenile polyposis syndrome (JPS) is a rare, autosomal dominant condition. The polyps predominate in the colon but may be seen less commonly in the stomach or small intestine. We report an unusual case of JPS associated with massive gastric polyposis, resulting in a giant stomach, severe anemia, hematemesis, protein-losing enteropathy, and gastric outlet obstruction. Progressive complications ultimately necessitated a total gastrectomy.

Case

A 27-year-old woman presented in 2005 with severe anemia. Gastroscopy revealed severe gastric polyposis. Histopathology confirmed juvenile polyposis. Gastrectomy was initially declined. Progressive hematemesis, hypoproteinemia, and gastric outlet obstruction, however, resulted in a total gastrectomy 5 years following initial presentation. Massive gastric polyposis resulted in severe gastromegaly.

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Author information

Authors and Affiliations

  1. Department of Surgery, Mount Sinai Hospital, 600 University Avenue, Suite 1225, Toronto, ON, M5G 1X5, Canada

    Nathalie Wong-Chong & Judith Andrea McCart

  2. Department of Pathology and Laboratory Medicine, Mount Sinai Hospital, Toronto, ON, Canada

    Wondwossen Hailu Kidanewold & Richard Kirsch

  3. Department of Gastroenterology, St. Michael’s Hospital, Toronto, ON, Canada

    Gary Robert May

Authors
  1. Nathalie Wong-Chong
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  2. Wondwossen Hailu Kidanewold
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  3. Richard Kirsch
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  4. Gary Robert May
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  5. Judith Andrea McCart
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Corresponding author

Correspondence to Judith Andrea McCart.

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Consent

Written consent was obtained from the patient for the publication of the case and the clinical images. A copy of the written consent is available for review by the Editor-in-Chief of this journal.

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Wong-Chong, N., Kidanewold, W.H., Kirsch, R. et al. Giant Stomach Secondary to Juvenile Polyposis Syndrome. J Gastrointest Surg 16, 669–672 (2012). https://doi.org/10.1007/s11605-011-1714-4

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  • DOI: https://doi.org/10.1007/s11605-011-1714-4

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