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Clinical findings on ANCA-associated renal vasculitis from the Japan RPGN registry obtained via a questionnaire survey

  • Review Article
  • The Asia Pacific Meeting of Vasculitis and ANCA Workshop 2012
  • Published:
Clinical and Experimental Nephrology Aims and scope Submit manuscript

An Erratum to this article was published on 23 March 2013

Abstract

Renal involvement with significant organ damage is common in anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV). As a result, it is independently referred to ANCA-associated renal vasculitis. Clinically, ANCA-associated renal vasculitis is characterized by rapidly progressive glomerulonephritis. Pathologically, it is defined by pauci-immune type necrotizing and crescentic glomerulonephritis. According to previous reports from all over the world, the etiology, prevalence, and prognosis of RPGN including ANCA-associated renal vasculitis varies among races and periods. To elucidate the clinical characteristics of Japanese RPGN patients, a registry derived from a questionnaire survey was established in 1999 and maintained until 2006. As a result, 1,772 cases were collected, analyzed, and reported previously. In this mini-review, we outline the characteristic clinical findings of Japanese patients (Asian) with ANCA-associated renal vasculitis, based on the registry data.

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References

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Acknowledgments

This study was supported in part by a Grant-in-Aid for Progressive Renal Diseases Research, Research on Intractable Disease, from the Ministry of Health, Labour and Welfare of Japan.

Conflict of interest

We declare that we have no conflicts of interest.

Author information

Authors and Affiliations

  1. Department of Nephrology, Faculty of Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba, Ibaraki, 305-8575, Japan

    Kunihiro Yamagata & Joichi Usui

  2. Department of Medicine and Clinical Science, Okayama University Graduate School of Medicine, Dentistry, and Pharmaceutical Sciences, Okayama, Japan

    Hitoshi Sugiyama & Hirofumi Makino

  3. Department of Medicine, Kidney Center, Tokyo Women’s Medical University, Tokyo, Japan

    Kosaku Nitta

  4. Division of Nephrology, Kanazawa University Hospital, Kanazawa, Japan

    Takashi Wada

  5. Department of Nephrology and Dialysis, The Tazuke Kofukai Medical Research Institute, Kitano Hospital, Osaka, Japan

    Eri Muso

  6. First Department of Internal Medicine, Kyorin University School of Medicine, Tokyo, Japan

    Yoshihiro Arimura

  7. Department of Nephrology, Tsukuba Memorial Hospital, Tsukuba, Ibaraki, Japan

    Akio Koyama

  8. Department of Nephrology, Internal Medicine, Nagoya University Graduate School of Medicine, Nagoya, Japan

    Seiichi Matsuo

Authors
  1. Kunihiro Yamagata
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  2. Joichi Usui
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  3. Hitoshi Sugiyama
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  4. Kosaku Nitta
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  5. Takashi Wada
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  6. Eri Muso
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  7. Yoshihiro Arimura
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  8. Akio Koyama
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  9. Hirofumi Makino
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  10. Seiichi Matsuo
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Corresponding author

Correspondence to Kunihiro Yamagata.

Additional information

The members of The Japanese RPGN Study Group of Progressive Renal Disease are Kunihiro Yamagata, Hitoshi Sugiyama, Kosaku Nitta, Takashi Wada, Eri Muso, Yoshihiro Arimura, Akio Koyama, Hirofumi Makino, and Seiichi Matsuo.

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Yamagata, K., Usui, J., Sugiyama, H. et al. Clinical findings on ANCA-associated renal vasculitis from the Japan RPGN registry obtained via a questionnaire survey. Clin Exp Nephrol 17, 646–649 (2013). https://doi.org/10.1007/s10157-012-0740-1

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  • DOI: https://doi.org/10.1007/s10157-012-0740-1

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