SpringerLink
Log in

Extrakonaler solitärer fibröser Tumor der Orbita

Extraconal solitary fibrous tumor of the orbit

  • Kasuistiken
  • Published:
Der Ophthalmologe Aims and scope Submit manuscript

Zusammenfassung

Der solitäre fibröse Tumor (SFT) ist ein seltener Spindelzelltumor, der von spezialisierten Fibroblasten ausgeht. Er wurde zuerst in der Pleura beschrieben, dann aber im ganzen Körper einschließlich der Orbita. Der Tumor ist zumeist gutartig, aber maligne Entartung mit Rezidiv und Metastasierung wurde auch in einzelnen Fällen beobachtet. Die Therapie der Wahl ist die komplette Exzision. Wir berichten über einen 50-jährigen Patienten, bei dem ein SFT der Orbita über eine transkonjunktivale vordere Orbitotomie entfernt wurde. Der Patient ist 1,5 Jahre nach der Operation tumor- und beschwerdefrei.

Abstract

Solitary fibrous tumors (SFT) are rare spindle cell neoplasms derived from specialized fibroblasts. This tumor was first described in the pleura and later in the whole body including the orbit. Although an SFT is generally a benign tumor malignant transformation and metastasization have also been observed in a few cases. Complete excision is the therapy of choice. Here we report on a 50-year-old male patient whose orbital SFT was removed by transconjunctival anterior orbitotomy and 1.5 years after the operation the patient is recurrence and complaint-free.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Log in via an institution

Subscribe and save

Springer+ Basic
EUR 32.99 /Month
  • Get 10 units per month
  • Download Article/Chapter or Ebook
  • 1 Unit = 1 Article or 1 Chapter
  • Cancel anytime
Subscribe now

Buy Now

Price includes VAT (France)

Instant access to the full article PDF.

Institutional subscriptions

Abb. 1
Abb. 2
Abb. 3
Abb. 4

Literatur

  1. Bernardini FP, Conciliis C de, Schneider S et al (2003) Solitary fibrous tumor of the orbit: is it rare? Report of a case series and review of the literature. Ophthalmology 110:1442–1448

    Article  PubMed  Google Scholar 

  2. Carrera M, Prat J, Quintana M (2001) Malignant solitary fibrous tumour of the orbit: report of a case with 8 years follow up. Eye 15:102–104

    Article  PubMed  CAS  Google Scholar 

  3. Cassarino DS, Auerbach A, Rushing EJ (2003) Widely invasive solitary fibrous tumour of the sphenoid sinus, cavernous sinus and pituitary fossa. Ann Diagn Pathol 7:169–173

    Article  PubMed  Google Scholar 

  4. Fletcher CDM (2006) The evolving classification of soft tissue tumours: an update based on the new WHO classification. Histopathology 26:557–563

    Google Scholar 

  5. Furusato E, Valenzuela IA, Fanburg-Smith JC et al (2011) Orbital solitary fibrous tumour: encompassing terminology for hemangiopericytoma, giant cell angiofibroma, and fibrous histiocytoma of the orbit: reappraisal of 41 cases. Hum Pathol 42:120–128

    Article  PubMed  Google Scholar 

  6. Guillou L, Lebhard S, Coindre JM (2000) Orbital and extraorbital giant cell angiofibroma: a giant cell-rich variant of solitary fibrous tumour? Clinicopathologic and immunohistochemical analysis of a series in favour of a unifying concept. Am J Surg Pathol 24:971–979

    Article  PubMed  CAS  Google Scholar 

  7. Krishnakumar S, Subramanian N, Mohan ER et al (2003) Solitary fibrous tumour of the orbit: a clinicopathologic study of six cases with review of the literature. Surv Ophthalmol 48:544–554

    Article  PubMed  Google Scholar 

  8. Manolusaridis K, Stropahl G, Guthoff RF (2011) Rezidivierender maligner solitärer fibröser Tumor der Orbita. Ophthalmologe 108:260–264

    Article  Google Scholar 

  9. Mullins JB, Holds JB, Branham GH, Thomas JR (1997) Complication of the transconjunctival approach: a review of 400 cases. Arch Otolaryngol Head Neck Surg 123:385–388

    PubMed  CAS  Google Scholar 

  10. Westra WH, Gerald W, Rosai J (1994) Solitary fibrous tumour. Consistent CD34 immunoreactivity and occurrence in the orbit. Am J Surg Pathol 18:992–998

    Article  PubMed  CAS  Google Scholar 

Download references

Interessenkonflikt

Der korrespondierende Autor gibt für sich und seine Koautoren an, dass kein Interessenkonflikt besteht.

Author information

Authors and Affiliations

  1. Augenklinik Detmold, Elisabethstr. 85, 32756, Detmold, Deutschland

    E. von Lovenberg

  2. Institut für Pathologie, Klinik Lippe-Detmold, Lippe-Detmold, Deutschland

    O. Kedziora & H.K. Wolf

  3. Institut für Pathologie und Neuropathologie, Universitätsklinikum Essen, Essen, Deutschland

    A. Bankfalvi

Authors
  1. E. von Lovenberg
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. O. Kedziora
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. H.K. Wolf
    View author publications

    You can also search for this author in PubMed Google Scholar

  4. A. Bankfalvi
    View author publications

    You can also search for this author in PubMed Google Scholar

Corresponding author

Correspondence to E. von Lovenberg.

Rights and permissions

Reprints and permissions

About this article

Cite this article

von Lovenberg, E., Kedziora, O., Wolf, H. et al. Extrakonaler solitärer fibröser Tumor der Orbita. Ophthalmologe 110, 357–359 (2013). https://doi.org/10.1007/s00347-012-2655-3

Download citation

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s00347-012-2655-3

Schlüsselwörter

Keywords

Search

Navigation